Cargando…

Lung transplantation in telomerase mutation carriers with pulmonary fibrosis

Lung transplantation is the only intervention that prolongs survival in idiopathic pulmonary fibrosis (IPF). Telomerase mutations are the most common identifiable genetic cause of IPF, and at times, the telomere defect manifests in extrapulmonary disease such as bone marrow failure. The relevance of...

Descripción completa

Detalles Bibliográficos
Autores principales: Silhan, Leann L., Shah, Pali D., Chambers, Daniel C., Snyder, Laurie D., Riise, Gerdt C., Wagner, Christa L., Hellström-Lindberg, Eva, Orens, Jonathan B., Mewton, Juliette F., Danoff, Sonye K., Arcasoy, Murat O., Armanios, Mary
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4076528/
https://www.ncbi.nlm.nih.gov/pubmed/24833766
http://dx.doi.org/10.1183/09031936.00060014

Ejemplares similares