Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys

Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease. It is characterized by progressive cyst formation in both kidneys, often leading to end-stage kidney disease. Indications for surgical removal of an ADPKD kidney include intractable pain, hematuria, in...

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Autores principales: Spithoven, Edwin M., Casteleijn, Niek F., Berger, Paul, Goldschmeding, Roel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2014
Materias:
Published online: June, 2014
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4086038/
https://www.ncbi.nlm.nih.gov/pubmed/25028584
http://dx.doi.org/10.1159/000363378
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author Spithoven, Edwin M.
Casteleijn, Niek F.
Berger, Paul
Goldschmeding, Roel
author_facet Spithoven, Edwin M.
Casteleijn, Niek F.
Berger, Paul
Goldschmeding, Roel
author_sort Spithoven, Edwin M.
collection PubMed
description Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease. It is characterized by progressive cyst formation in both kidneys, often leading to end-stage kidney disease. Indications for surgical removal of an ADPKD kidney include intractable pain, hematuria, infection, or exceptional enlargement and small abdominal cavity hampering implantation of a donor kidney. We report the case of an extraordinarily large ADPKD kidney weighing 8.7 kg (19.3 lb) with a maximal length of 48 cm (19 inch), and with cysts filled with both clear and bloody fluid.
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spelling pubmed-40860382014-07-15 Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys Spithoven, Edwin M. Casteleijn, Niek F. Berger, Paul Goldschmeding, Roel Case Rep Nephrol Urol Published online: June, 2014 Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease. It is characterized by progressive cyst formation in both kidneys, often leading to end-stage kidney disease. Indications for surgical removal of an ADPKD kidney include intractable pain, hematuria, infection, or exceptional enlargement and small abdominal cavity hampering implantation of a donor kidney. We report the case of an extraordinarily large ADPKD kidney weighing 8.7 kg (19.3 lb) with a maximal length of 48 cm (19 inch), and with cysts filled with both clear and bloody fluid. S. Karger AG 2014-06-04 /pmc/articles/PMC4086038/ /pubmed/25028584 http://dx.doi.org/10.1159/000363378 Text en Copyright © 2014 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article licensed under the terms of the Creative Commons Attribution-NonCommercial 3.0 Unported license (CC BY-NC) (www.karger.com/OA-license), applicable to the online version of the article only. Users may download, print and share this work on the Internet for noncommercial purposes only, provided the original work is properly cited, and a link to the original work on http://www.karger.com and the terms of this license are included in any shared versions.
spellingShingle Published online: June, 2014
Spithoven, Edwin M.
Casteleijn, Niek F.
Berger, Paul
Goldschmeding, Roel
Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys
title Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys
title_full Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys
title_fullStr Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys
title_full_unstemmed Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys
title_short Nephrectomy in Autosomal Dominant Polycystic Kidney Disease: A Patient with Exceptionally Large, Still Functioning Kidneys
title_sort nephrectomy in autosomal dominant polycystic kidney disease: a patient with exceptionally large, still functioning kidneys
topic Published online: June, 2014
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4086038/
https://www.ncbi.nlm.nih.gov/pubmed/25028584
http://dx.doi.org/10.1159/000363378
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