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Maxillary Melanotic Neuroectodermal Tumor of Infancy
The melanotic neuroectodermal tumor of infancy (MNTI) is a rare benign neoplasm of neural crest origin most commonly found in the anterior region of the maxilla. The tumor almost always develops during the first year of life, although in some cases it can be present at birth. MNTI’s present as a rap...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Jaypee Brothers Medical Publishers
2009
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4086571/ https://www.ncbi.nlm.nih.gov/pubmed/25206125 http://dx.doi.org/10.5005/jp-journals-10005-1021 |
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author | A da Fonseca, Marcio Thikkurissy, S |
author_facet | A da Fonseca, Marcio Thikkurissy, S |
author_sort | A da Fonseca, Marcio |
collection | PubMed |
description | The melanotic neuroectodermal tumor of infancy (MNTI) is a rare benign neoplasm of neural crest origin most commonly found in the anterior region of the maxilla. The tumor almost always develops during the first year of life, although in some cases it can be present at birth. MNTI’s present as a rapidly growing, painless expansile, partly pigmented mass. They are usually unencapsulated, with a tendency to occur as a single lesion. Local excision is the treatment of choice and is usually curative. Main sites for recurrences are the maxilla (57%) and the skull/brain (28.6%). Malignant transformation has been noted in approximately 6.5% of all cases and in 2% of maxillary tumors. The case of a 3-month old boy who presented with a loose primary maxillary left central incisor is discussed. The diagnostic and clinico-pathological features as well as tumor management and importance of a timely diagnosis are reviewed. |
format | Online Article Text |
id | pubmed-4086571 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2009 |
publisher | Jaypee Brothers Medical Publishers |
record_format | MEDLINE/PubMed |
spelling | pubmed-40865712014-09-09 Maxillary Melanotic Neuroectodermal Tumor of Infancy A da Fonseca, Marcio Thikkurissy, S Int J Clin Pediatr Dent Case Report The melanotic neuroectodermal tumor of infancy (MNTI) is a rare benign neoplasm of neural crest origin most commonly found in the anterior region of the maxilla. The tumor almost always develops during the first year of life, although in some cases it can be present at birth. MNTI’s present as a rapidly growing, painless expansile, partly pigmented mass. They are usually unencapsulated, with a tendency to occur as a single lesion. Local excision is the treatment of choice and is usually curative. Main sites for recurrences are the maxilla (57%) and the skull/brain (28.6%). Malignant transformation has been noted in approximately 6.5% of all cases and in 2% of maxillary tumors. The case of a 3-month old boy who presented with a loose primary maxillary left central incisor is discussed. The diagnostic and clinico-pathological features as well as tumor management and importance of a timely diagnosis are reviewed. Jaypee Brothers Medical Publishers 2009 2009-12-26 /pmc/articles/PMC4086571/ /pubmed/25206125 http://dx.doi.org/10.5005/jp-journals-10005-1021 Text en Copyright © 2009; Jaypee Brothers Medical Publishers (P) Ltd. This work is licensed under a Creative Commons Attribution 3.0 Unported License. To view a copy of this license, visit http://creativecommons.org/licenses/by/3.0/ |
spellingShingle | Case Report A da Fonseca, Marcio Thikkurissy, S Maxillary Melanotic Neuroectodermal Tumor of Infancy |
title | Maxillary Melanotic Neuroectodermal
Tumor of Infancy |
title_full | Maxillary Melanotic Neuroectodermal
Tumor of Infancy |
title_fullStr | Maxillary Melanotic Neuroectodermal
Tumor of Infancy |
title_full_unstemmed | Maxillary Melanotic Neuroectodermal
Tumor of Infancy |
title_short | Maxillary Melanotic Neuroectodermal
Tumor of Infancy |
title_sort | maxillary melanotic neuroectodermal
tumor of infancy |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4086571/ https://www.ncbi.nlm.nih.gov/pubmed/25206125 http://dx.doi.org/10.5005/jp-journals-10005-1021 |
work_keys_str_mv | AT adafonsecamarcio maxillarymelanoticneuroectodermaltumorofinfancy AT thikkurissys maxillarymelanoticneuroectodermaltumorofinfancy |