Huge Facial Desmoid Tumors with Neck Extension: A Case Report

INTRODUCTION: Desmoid tumors are very rare, benign fibrous neoplasms arise from the musculoaponeurotic structures throughout the body. CASE REPORT: The patient was a seven-year old boy with a large mandibular mass growing over a period of six months. His CT-scan showed a large mass, 13 cm in diamete...

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Autores principales: Ghazipour, Ali, Ghavami Lahiji, Shervin, Bradd, Bassel, Saleheh, Fariborz
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Mashhad University of Medical Sciences 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4087860/
https://www.ncbi.nlm.nih.gov/pubmed/25009811
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author Ghazipour, Ali
Ghavami Lahiji, Shervin
Bradd, Bassel
Saleheh, Fariborz
author_facet Ghazipour, Ali
Ghavami Lahiji, Shervin
Bradd, Bassel
Saleheh, Fariborz
author_sort Ghazipour, Ali
collection PubMed
description INTRODUCTION: Desmoid tumors are very rare, benign fibrous neoplasms arise from the musculoaponeurotic structures throughout the body. CASE REPORT: The patient was a seven-year old boy with a large mandibular mass growing over a period of six months. His CT-scan showed a large mass, 13 cm in diameter in the cheek area extending to the neck and trachea. Biopsy was compatible with desmoid fibromatosis. He was given neoadjovant treatment with vinblastin and methotrexate. The patient underwent a tracheostomy. Then a complete hemimandibulectomy and submandibular gland excision was performed. Finally reconstruction with latisimus dorsi free flap was performed. CONCLUSION: Despite rarity desmoid tumors should be kept in mind of an otorhinolaryngologist as a differential diagnosis in children with head and neck mass.
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spelling pubmed-40878602014-07-09 Huge Facial Desmoid Tumors with Neck Extension: A Case Report Ghazipour, Ali Ghavami Lahiji, Shervin Bradd, Bassel Saleheh, Fariborz Iran J Otorhinolaryngol Case Report INTRODUCTION: Desmoid tumors are very rare, benign fibrous neoplasms arise from the musculoaponeurotic structures throughout the body. CASE REPORT: The patient was a seven-year old boy with a large mandibular mass growing over a period of six months. His CT-scan showed a large mass, 13 cm in diameter in the cheek area extending to the neck and trachea. Biopsy was compatible with desmoid fibromatosis. He was given neoadjovant treatment with vinblastin and methotrexate. The patient underwent a tracheostomy. Then a complete hemimandibulectomy and submandibular gland excision was performed. Finally reconstruction with latisimus dorsi free flap was performed. CONCLUSION: Despite rarity desmoid tumors should be kept in mind of an otorhinolaryngologist as a differential diagnosis in children with head and neck mass. Mashhad University of Medical Sciences 2014-07 /pmc/articles/PMC4087860/ /pubmed/25009811 Text en This is an Open Access article distributed under the terms of the Creative Commons Attribution License, (http://creativecommons.org/licenses/by/3.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Ghazipour, Ali
Ghavami Lahiji, Shervin
Bradd, Bassel
Saleheh, Fariborz
Huge Facial Desmoid Tumors with Neck Extension: A Case Report
title Huge Facial Desmoid Tumors with Neck Extension: A Case Report
title_full Huge Facial Desmoid Tumors with Neck Extension: A Case Report
title_fullStr Huge Facial Desmoid Tumors with Neck Extension: A Case Report
title_full_unstemmed Huge Facial Desmoid Tumors with Neck Extension: A Case Report
title_short Huge Facial Desmoid Tumors with Neck Extension: A Case Report
title_sort huge facial desmoid tumors with neck extension: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4087860/
https://www.ncbi.nlm.nih.gov/pubmed/25009811
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AT salehehfariborz hugefacialdesmoidtumorswithneckextensionacasereport

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