Primary desmoplastic small round cell tumor of the duodenum

The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray re...

Descripción completa

Detalles Bibliográficos
Autores principales: Liu, Qi, Liu, Nan, Chen, DeXing
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4096735/
https://www.ncbi.nlm.nih.gov/pubmed/24997683
http://dx.doi.org/10.1186/2047-783X-19-38
_version_ 1782326171820621824
author Liu, Qi
Liu, Nan
Chen, DeXing
author_facet Liu, Qi
Liu, Nan
Chen, DeXing
author_sort Liu, Qi
collection PubMed
description The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.
format Online
Article
Text
id pubmed-4096735
institution National Center for Biotechnology Information
language English
publishDate 2014
publisher BioMed Central
record_format MEDLINE/PubMed
spelling pubmed-40967352014-07-16 Primary desmoplastic small round cell tumor of the duodenum Liu, Qi Liu, Nan Chen, DeXing Eur J Med Res Case Report The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease. BioMed Central 2014-07-06 /pmc/articles/PMC4096735/ /pubmed/24997683 http://dx.doi.org/10.1186/2047-783X-19-38 Text en Copyright © 2014 Liu et al.; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly credited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Liu, Qi
Liu, Nan
Chen, DeXing
Primary desmoplastic small round cell tumor of the duodenum
title Primary desmoplastic small round cell tumor of the duodenum
title_full Primary desmoplastic small round cell tumor of the duodenum
title_fullStr Primary desmoplastic small round cell tumor of the duodenum
title_full_unstemmed Primary desmoplastic small round cell tumor of the duodenum
title_short Primary desmoplastic small round cell tumor of the duodenum
title_sort primary desmoplastic small round cell tumor of the duodenum
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4096735/
https://www.ncbi.nlm.nih.gov/pubmed/24997683
http://dx.doi.org/10.1186/2047-783X-19-38
work_keys_str_mv AT liuqi primarydesmoplasticsmallroundcelltumoroftheduodenum
AT liunan primarydesmoplasticsmallroundcelltumoroftheduodenum
AT chendexing primarydesmoplasticsmallroundcelltumoroftheduodenum

Ejemplares similares