Cargando…

Juvenile xanthogranuloma: a rare benign histiocytic disorder

Juvenile xanthogranuloma (JXG) is a rare histiocytic disorder that typically affects children. The clinical presentation of this disease is characterized by single or, rarely, multiple yellow and brown skin nodules, most often found on the face and neck. Internal organ involvement has been sporadica...

Descripción completa

Detalles Bibliográficos
Autores principales: Szczerkowska-Dobosz, Aneta, Kozicka, Dorota, Purzycka-Bohdan, Dorota, Biernat, Wojciech, Stawczyk, Marta, Nowicki, Roman
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Termedia Publishing House 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4112258/
https://www.ncbi.nlm.nih.gov/pubmed/25097495
http://dx.doi.org/10.5114/pdia.2014.40918
Descripción
Sumario:Juvenile xanthogranuloma (JXG) is a rare histiocytic disorder that typically affects children. The clinical presentation of this disease is characterized by single or, rarely, multiple yellow and brown skin nodules, most often found on the face and neck. Internal organ involvement has been sporadically observed in JXG and is associated with an increased risk of serious complications. We report two cases with a small and large nodular form of JXG.