Dysregulation of matricellular proteins is an early signature of pathology in laminin-deficient muscular dystrophy

BACKGROUND: MDC1A is a congenital neuromuscular disorder with developmentally complex and progressive pathologies that results from a deficiency in the protein laminin α(2). MDC1A is associated with a multitude of pathologies, including increased apoptosis, inflammation and fibrosis. In order to ass...

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Detalles Bibliográficos
Autores principales: Mehuron, Thomas, Kumar, Ajay, Duarte, Lina, Yamauchi, Jenny, Accorsi, Anthony, Girgenrath, Mahasweta
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Research
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4114446/
https://www.ncbi.nlm.nih.gov/pubmed/25075272
http://dx.doi.org/10.1186/2044-5040-4-14

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4114446/
https://www.ncbi.nlm.nih.gov/pubmed/25075272
http://dx.doi.org/10.1186/2044-5040-4-14

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