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A 55 years old man with pulmonary alveolar microlithiasis

Pulmonary alveolar microlithiasis (PAM) is a very rare diffuse chronic lung disease characterized by deposition of small spherules of calcium phosphate within the alveolar cavity. The disease is usually seen from birth up to 40 years of age and is usually diagnosed incidentally during radiography of...

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Autores principales: Saeed, Rebeen R., Ali, Kosar M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4129609/
https://www.ncbi.nlm.nih.gov/pubmed/25125824
http://dx.doi.org/10.4103/0970-2113.135786
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author Saeed, Rebeen R.
Ali, Kosar M.
author_facet Saeed, Rebeen R.
Ali, Kosar M.
author_sort Saeed, Rebeen R.
collection PubMed
description Pulmonary alveolar microlithiasis (PAM) is a very rare diffuse chronic lung disease characterized by deposition of small spherules of calcium phosphate within the alveolar cavity. The disease is usually seen from birth up to 40 years of age and is usually diagnosed incidentally during radiography of the chest for other reasons. Most of patients are asymptomatic or having very mild symptoms and the majority of patients either have normal or restrictive pulmonary function test. Clinically, the course of the disease is different; it remains static in few patients or it may progress to pulmonary fibrosis, respiratory failure and cor pulmonale in others. In this case report, we present a 55-year-old man who presented with moderate shortness of breath which has progressed from mild symptoms with in the previous years. His chest high-resolution CT scan showed diffusely scattered, ill-defined little shadowy micronodules which involve the left lung; lingula and left lower lobe in particular. A lung biopsy confirmed the diagnosis of PAM. He was followed up for 1 year with treatment by steroid and alendronate, and no progression was noticed in fact improvement in pulmonary function test noticed. This is the first case report of PAM in Kurdistan.
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spelling pubmed-41296092014-08-14 A 55 years old man with pulmonary alveolar microlithiasis Saeed, Rebeen R. Ali, Kosar M. Lung India Case Report Pulmonary alveolar microlithiasis (PAM) is a very rare diffuse chronic lung disease characterized by deposition of small spherules of calcium phosphate within the alveolar cavity. The disease is usually seen from birth up to 40 years of age and is usually diagnosed incidentally during radiography of the chest for other reasons. Most of patients are asymptomatic or having very mild symptoms and the majority of patients either have normal or restrictive pulmonary function test. Clinically, the course of the disease is different; it remains static in few patients or it may progress to pulmonary fibrosis, respiratory failure and cor pulmonale in others. In this case report, we present a 55-year-old man who presented with moderate shortness of breath which has progressed from mild symptoms with in the previous years. His chest high-resolution CT scan showed diffusely scattered, ill-defined little shadowy micronodules which involve the left lung; lingula and left lower lobe in particular. A lung biopsy confirmed the diagnosis of PAM. He was followed up for 1 year with treatment by steroid and alendronate, and no progression was noticed in fact improvement in pulmonary function test noticed. This is the first case report of PAM in Kurdistan. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC4129609/ /pubmed/25125824 http://dx.doi.org/10.4103/0970-2113.135786 Text en Copyright: © Lung India http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Saeed, Rebeen R.
Ali, Kosar M.
A 55 years old man with pulmonary alveolar microlithiasis
title A 55 years old man with pulmonary alveolar microlithiasis
title_full A 55 years old man with pulmonary alveolar microlithiasis
title_fullStr A 55 years old man with pulmonary alveolar microlithiasis
title_full_unstemmed A 55 years old man with pulmonary alveolar microlithiasis
title_short A 55 years old man with pulmonary alveolar microlithiasis
title_sort 55 years old man with pulmonary alveolar microlithiasis
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4129609/
https://www.ncbi.nlm.nih.gov/pubmed/25125824
http://dx.doi.org/10.4103/0970-2113.135786
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