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Biophysical Characterisation of Calumenin as a Charged F508del-CFTR Folding Modulator

The cystic fibrosis transmembrane regulator (CFTR) is a cyclic-AMP dependent chloride channel expressed at the apical surface of epithelial cells lining various organs such as the respiratory tract. Defective processing and functioning of this protein caused by mutations in the CFTR gene results in...

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Detalles Bibliográficos
Autores principales:	Tripathi, Rashmi, Benz, Nathalie, Culleton, Bridget, Trouvé, Pascal, Férec, Claude
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2014
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4132023/ https://www.ncbi.nlm.nih.gov/pubmed/25120007 http://dx.doi.org/10.1371/journal.pone.0104970

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