Cargando…

Pleuropulmonary Blastoma: A Case Report and Review of the Literature

The case of 38-month-old boy is being reported who was brought to the pediatrics clinic with fever, cough, hemoptysis, and breathing difficulty. Imaging studies revealed a right lower chest mass. Lobectomy and histopathological examination revealed it to be predominantly solid pleuropulmonary blasto...

Descripción completa

Detalles Bibliográficos
Autores principales: Khan, Amjad Ali, El-Borai, Ahmed Kamal, Alnoaiji, Mohammad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4142298/
https://www.ncbi.nlm.nih.gov/pubmed/25177506
http://dx.doi.org/10.1155/2014/509086
_version_ 1782331754805198848
author Khan, Amjad Ali
El-Borai, Ahmed Kamal
Alnoaiji, Mohammad
author_facet Khan, Amjad Ali
El-Borai, Ahmed Kamal
Alnoaiji, Mohammad
author_sort Khan, Amjad Ali
collection PubMed
description The case of 38-month-old boy is being reported who was brought to the pediatrics clinic with fever, cough, hemoptysis, and breathing difficulty. Imaging studies revealed a right lower chest mass. Lobectomy and histopathological examination revealed it to be predominantly solid pleuropulmonary blastoma type II. It is a rare pediatric pleuropulmonary tumor with aggressive behavior and tendency to spread to the brain. The case is being presented to make the general histopathologist aware of this rare entity and to highlight to the pediatric physicians/surgeons, radiologists, and histopathologists the fact that lung cysts in infants and young children should be evaluated seriously and sampled thoroughly to diagnose cases of type I pleuropulmonary blastoma which will progress over time to type II or type III tumors. Also the siblings and first degree relatives of the patient should be screened for associated pulmonary and extrapulmonary benign and malignant conditions.
format Online
Article
Text
id pubmed-4142298
institution National Center for Biotechnology Information
language English
publishDate 2014
publisher Hindawi Publishing Corporation
record_format MEDLINE/PubMed
spelling pubmed-41422982014-08-31 Pleuropulmonary Blastoma: A Case Report and Review of the Literature Khan, Amjad Ali El-Borai, Ahmed Kamal Alnoaiji, Mohammad Case Rep Pathol Case Report The case of 38-month-old boy is being reported who was brought to the pediatrics clinic with fever, cough, hemoptysis, and breathing difficulty. Imaging studies revealed a right lower chest mass. Lobectomy and histopathological examination revealed it to be predominantly solid pleuropulmonary blastoma type II. It is a rare pediatric pleuropulmonary tumor with aggressive behavior and tendency to spread to the brain. The case is being presented to make the general histopathologist aware of this rare entity and to highlight to the pediatric physicians/surgeons, radiologists, and histopathologists the fact that lung cysts in infants and young children should be evaluated seriously and sampled thoroughly to diagnose cases of type I pleuropulmonary blastoma which will progress over time to type II or type III tumors. Also the siblings and first degree relatives of the patient should be screened for associated pulmonary and extrapulmonary benign and malignant conditions. Hindawi Publishing Corporation 2014 2014-08-07 /pmc/articles/PMC4142298/ /pubmed/25177506 http://dx.doi.org/10.1155/2014/509086 Text en Copyright © 2014 Amjad Ali Khan et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Khan, Amjad Ali
El-Borai, Ahmed Kamal
Alnoaiji, Mohammad
Pleuropulmonary Blastoma: A Case Report and Review of the Literature
title Pleuropulmonary Blastoma: A Case Report and Review of the Literature
title_full Pleuropulmonary Blastoma: A Case Report and Review of the Literature
title_fullStr Pleuropulmonary Blastoma: A Case Report and Review of the Literature
title_full_unstemmed Pleuropulmonary Blastoma: A Case Report and Review of the Literature
title_short Pleuropulmonary Blastoma: A Case Report and Review of the Literature
title_sort pleuropulmonary blastoma: a case report and review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4142298/
https://www.ncbi.nlm.nih.gov/pubmed/25177506
http://dx.doi.org/10.1155/2014/509086
work_keys_str_mv AT khanamjadali pleuropulmonaryblastomaacasereportandreviewoftheliterature
AT elboraiahmedkamal pleuropulmonaryblastomaacasereportandreviewoftheliterature
AT alnoaijimohammad pleuropulmonaryblastomaacasereportandreviewoftheliterature