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Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report
Nevoid basal cell carcinoma syndrome is a syndrome with wide variety of manifestations ranging from oral lesions to skeletal deformities. It calls for due responsibility of maxillofacial surgeon to diagnose the syndrome because very often they are the first health professionals to see the patient fo...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2014
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4147827/ https://www.ncbi.nlm.nih.gov/pubmed/25191087 http://dx.doi.org/10.4103/0976-237X.137980 |
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author | Kulkarni, Gayithri Harish Khaji, Shahanavaj I. Metkari, Suryakant Kulkarni, Harish S. Kulkarni, Reshma |
author_facet | Kulkarni, Gayithri Harish Khaji, Shahanavaj I. Metkari, Suryakant Kulkarni, Harish S. Kulkarni, Reshma |
author_sort | Kulkarni, Gayithri Harish |
collection | PubMed |
description | Nevoid basal cell carcinoma syndrome is a syndrome with wide variety of manifestations ranging from oral lesions to skeletal deformities. It calls for due responsibility of maxillofacial surgeon to diagnose the syndrome because very often they are the first health professionals to see the patient for the treatment of keratocystic odontogenic tumor. Keratocystic odontogenic tumor has been the topic of numerous investigators, is known for its potentially aggressive behavior, significant rate of recurrences. KCOT often occurs as a solitary lesion, in some instances multiple keratocysts may occur in association with a syndrome called Gorlin-Goltz syndrome (nevoid BCC, jaw cyst bifid rib basal cell nevus syndrome). Here, we present a case of multiple keratocysts in the mandible in association with skeletal, ocular, cutaneous anomalies in the given clinical scenario, which has profound relevance in the clinical dental practice. |
format | Online Article Text |
id | pubmed-4147827 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-41478272014-09-04 Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report Kulkarni, Gayithri Harish Khaji, Shahanavaj I. Metkari, Suryakant Kulkarni, Harish S. Kulkarni, Reshma Contemp Clin Dent Case Report Nevoid basal cell carcinoma syndrome is a syndrome with wide variety of manifestations ranging from oral lesions to skeletal deformities. It calls for due responsibility of maxillofacial surgeon to diagnose the syndrome because very often they are the first health professionals to see the patient for the treatment of keratocystic odontogenic tumor. Keratocystic odontogenic tumor has been the topic of numerous investigators, is known for its potentially aggressive behavior, significant rate of recurrences. KCOT often occurs as a solitary lesion, in some instances multiple keratocysts may occur in association with a syndrome called Gorlin-Goltz syndrome (nevoid BCC, jaw cyst bifid rib basal cell nevus syndrome). Here, we present a case of multiple keratocysts in the mandible in association with skeletal, ocular, cutaneous anomalies in the given clinical scenario, which has profound relevance in the clinical dental practice. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC4147827/ /pubmed/25191087 http://dx.doi.org/10.4103/0976-237X.137980 Text en Copyright: © Contemporary Clinical Dentistry http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Kulkarni, Gayithri Harish Khaji, Shahanavaj I. Metkari, Suryakant Kulkarni, Harish S. Kulkarni, Reshma Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report |
title | Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report |
title_full | Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report |
title_fullStr | Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report |
title_full_unstemmed | Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report |
title_short | Multiple keratocysts of the mandible in association with Gorlin-Goltz syndrome: A rare case report |
title_sort | multiple keratocysts of the mandible in association with gorlin-goltz syndrome: a rare case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4147827/ https://www.ncbi.nlm.nih.gov/pubmed/25191087 http://dx.doi.org/10.4103/0976-237X.137980 |
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