Upper Respiratory System Involvement as the Only Manifestation of Granulomatosis with Polyangiitis in a Child with Marfan Phenotype

We report a 9-year old girl with an unusual presentation of granulomatosis with polyangiitis in association with Marfan phenotype. The patient presented with recurrent sinusitis, epistaxis, hearing loss and hyperplastic gingivitis, without any signs or symptoms of major organ involvement.

Detalles Bibliográficos
Autores principales: Amin, Reza, Alyasin, Soheila, Momen, Tooba, Khoshkhouy, Maryam, Darougar, Sepideh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: National Research Institute of Tuberculosis and Lung Disease 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4153231/
https://www.ncbi.nlm.nih.gov/pubmed/25191453
Descripción
Sumario:We report a 9-year old girl with an unusual presentation of granulomatosis with polyangiitis in association with Marfan phenotype. The patient presented with recurrent sinusitis, epistaxis, hearing loss and hyperplastic gingivitis, without any signs or symptoms of major organ involvement.

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