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The value of respiratory muscle testing in a child with congenital muscular dystrophy

Respiratory muscle testing is often limited to noninvasive volitional tests such as vital capacity and maximal static pressures. We report the case of a 12-year-old boy with congenital muscular dystrophy (CMD) in whom invasive and non-volitional respiratory muscle tests showed an elective diaphragma...

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Detalles Bibliográficos
Autores principales:	Khirani, Sonia, Dabaj, Ivana, Amaddeo, Alessandro, Ramirez, Adriana, Quijano-Roy, Susana, Fauroux, Brigitte
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BlackWell Publishing Ltd 2014
Materias:	Case Reports
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4184737/ https://www.ncbi.nlm.nih.gov/pubmed/25473580 http://dx.doi.org/10.1002/rcr2.61

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