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X-linked Hyper-IgM Syndrome with Bronchiectasis

The X-linked hyper-immunoglobulin M syndrome (HIGM-1) is a rare genetic disorder characterized by elevated serum IgM levels and low to undetectable levels of serum IgG, IgA and IgE. These patients characteristically present with recurrent sinopulmonary infections and recurrent diarrhea. They also ha...

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Detalles Bibliográficos
Autores principales:	Nandan, Devki, Nag, Vimal Kumar, Trivedi, Nitin, Singh, Sarman
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Medknow Publications & Media Pvt Ltd 2014
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4196358/ https://www.ncbi.nlm.nih.gov/pubmed/25328337 http://dx.doi.org/10.4103/0974-2727.141510

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