Correction of aortic coarctation in a girl with severe PHACE syndrome

A 12-year-old Chinese girl was demonstrated multivessel distortion and malformation: aortic coarctation with the narrowest lumen diameter measuring of 4 mm located between the left common carotid artery and the left subclavian artery, a huge and thin-walled aneurysm is connected to the coarctation,...

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Autores principales: Xiong, Lian, Xia, Zhenkun, Fan, Chengming, Zhang, Weizhi, Yang, Jinfu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4203972/
https://www.ncbi.nlm.nih.gov/pubmed/25312304
http://dx.doi.org/10.1186/s13019-014-0169-6
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author Xiong, Lian
Xia, Zhenkun
Fan, Chengming
Zhang, Weizhi
Yang, Jinfu
author_facet Xiong, Lian
Xia, Zhenkun
Fan, Chengming
Zhang, Weizhi
Yang, Jinfu
author_sort Xiong, Lian
collection PubMed
description A 12-year-old Chinese girl was demonstrated multivessel distortion and malformation: aortic coarctation with the narrowest lumen diameter measuring of 4 mm located between the left common carotid artery and the left subclavian artery, a huge and thin-walled aneurysm is connected to the coarctation, and the descending aorta was distorted. Cerebrovascular revealed distorted arteries and a completely aberrant brain blood supply. She underwent correction of the aortic coarctation by establishing a bypass between the ascending aorta and the descending aorta using a 13-mm Gore-tex tube. Postoperative recovery was uneventful, at 6-month follow-up, the cervical vascular pulsatility was relieved and she is in good condition. ELECTRONIC SUPPLEMENTARY MATERIAL: The online version of this article (doi:10.1186/s13019-014-0169-6) contains supplementary material, which is available to authorized users.
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spelling pubmed-42039722014-10-22 Correction of aortic coarctation in a girl with severe PHACE syndrome Xiong, Lian Xia, Zhenkun Fan, Chengming Zhang, Weizhi Yang, Jinfu J Cardiothorac Surg Case Report A 12-year-old Chinese girl was demonstrated multivessel distortion and malformation: aortic coarctation with the narrowest lumen diameter measuring of 4 mm located between the left common carotid artery and the left subclavian artery, a huge and thin-walled aneurysm is connected to the coarctation, and the descending aorta was distorted. Cerebrovascular revealed distorted arteries and a completely aberrant brain blood supply. She underwent correction of the aortic coarctation by establishing a bypass between the ascending aorta and the descending aorta using a 13-mm Gore-tex tube. Postoperative recovery was uneventful, at 6-month follow-up, the cervical vascular pulsatility was relieved and she is in good condition. ELECTRONIC SUPPLEMENTARY MATERIAL: The online version of this article (doi:10.1186/s13019-014-0169-6) contains supplementary material, which is available to authorized users. BioMed Central 2014-10-14 /pmc/articles/PMC4203972/ /pubmed/25312304 http://dx.doi.org/10.1186/s13019-014-0169-6 Text en © Xiong et al.; licensee BioMed Central Ltd. 2014 This article is published under license to BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly credited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Xiong, Lian
Xia, Zhenkun
Fan, Chengming
Zhang, Weizhi
Yang, Jinfu
Correction of aortic coarctation in a girl with severe PHACE syndrome
title Correction of aortic coarctation in a girl with severe PHACE syndrome
title_full Correction of aortic coarctation in a girl with severe PHACE syndrome
title_fullStr Correction of aortic coarctation in a girl with severe PHACE syndrome
title_full_unstemmed Correction of aortic coarctation in a girl with severe PHACE syndrome
title_short Correction of aortic coarctation in a girl with severe PHACE syndrome
title_sort correction of aortic coarctation in a girl with severe phace syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4203972/
https://www.ncbi.nlm.nih.gov/pubmed/25312304
http://dx.doi.org/10.1186/s13019-014-0169-6
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AT zhangweizhi correctionofaorticcoarctationinagirlwithseverephacesyndrome
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