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Prions in Variably Protease-Sensitive Prionopathy: An Update
Human prion diseases, including sporadic, familial, and acquired forms such as Creutzfeldt-Jakob disease (CJD), are caused by prions in which an abnormal prion protein (PrP(Sc)) derived from its normal cellular isoform (PrP(C)) is the only known component. The recently-identified variably protease-s...
Autores principales: | Zou, Wen-Quan, Gambetti, Pierluigi, Xiao, Xiangzhu, Yuan, Jue, Langeveld, Jan, Pirisinu, Laura |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2013
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4235694/ https://www.ncbi.nlm.nih.gov/pubmed/25437202 http://dx.doi.org/10.3390/pathogens2030457 |
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