Cargando…

Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review

Neurofibromatosis type-I (NF-I) is an autosomal-dominant hereditary disorder, in which spinal skeletal deformities are one of the manifestations and manifest as acquired abnormalities and present as short, sharp, and angular (usually thoracic) curves. The scoliosis can be severe requiring surgical i...

Descripción completa

Detalles Bibliográficos
Autores principales: Bamps, Sven, Calenbergh, Frank Van, Loon, Johan Van, Paesschen, Raf Van, Vanderschot, Paul
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4244797/
https://www.ncbi.nlm.nih.gov/pubmed/25552858
http://dx.doi.org/10.4103/0976-3147.143208
_version_ 1782346279701970944
author Bamps, Sven
Calenbergh, Frank Van
Loon, Johan Van
Paesschen, Raf Van
Vanderschot, Paul
author_facet Bamps, Sven
Calenbergh, Frank Van
Loon, Johan Van
Paesschen, Raf Van
Vanderschot, Paul
author_sort Bamps, Sven
collection PubMed
description Neurofibromatosis type-I (NF-I) is an autosomal-dominant hereditary disorder, in which spinal skeletal deformities are one of the manifestations and manifest as acquired abnormalities and present as short, sharp, and angular (usually thoracic) curves. The scoliosis can be severe requiring surgical intervention. The surgical procedure can be difficult because of scalloping of the vertebral bodies and dural ectasia. We state that in selected cases of severe thoracic dystrophic kyphoscoliosis in NF-I, the posterolateral approach is the only possible method to visualize the anterior thoracic spinal cord, perform anterior decompression, and to stabilize the thoracic deformity, because of the anterior dural ectasias and the kyphosis limiting an anterior procedure.
format Online
Article
Text
id pubmed-4244797
institution National Center for Biotechnology Information
language English
publishDate 2015
publisher Medknow Publications & Media Pvt Ltd
record_format MEDLINE/PubMed
spelling pubmed-42447972015-01-01 Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review Bamps, Sven Calenbergh, Frank Van Loon, Johan Van Paesschen, Raf Van Vanderschot, Paul J Neurosci Rural Pract Case Report Neurofibromatosis type-I (NF-I) is an autosomal-dominant hereditary disorder, in which spinal skeletal deformities are one of the manifestations and manifest as acquired abnormalities and present as short, sharp, and angular (usually thoracic) curves. The scoliosis can be severe requiring surgical intervention. The surgical procedure can be difficult because of scalloping of the vertebral bodies and dural ectasia. We state that in selected cases of severe thoracic dystrophic kyphoscoliosis in NF-I, the posterolateral approach is the only possible method to visualize the anterior thoracic spinal cord, perform anterior decompression, and to stabilize the thoracic deformity, because of the anterior dural ectasias and the kyphosis limiting an anterior procedure. Medknow Publications & Media Pvt Ltd 2015 /pmc/articles/PMC4244797/ /pubmed/25552858 http://dx.doi.org/10.4103/0976-3147.143208 Text en Copyright: © Journal of Neurosciences in Rural Practice http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Bamps, Sven
Calenbergh, Frank Van
Loon, Johan Van
Paesschen, Raf Van
Vanderschot, Paul
Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review
title Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review
title_full Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review
title_fullStr Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review
title_full_unstemmed Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review
title_short Posterolateral approach in a neurofibromatosis type-I patient with severe dystrophic thoracic kyphoscoliosis: A case report, cadaver study, and literature review
title_sort posterolateral approach in a neurofibromatosis type-i patient with severe dystrophic thoracic kyphoscoliosis: a case report, cadaver study, and literature review
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4244797/
https://www.ncbi.nlm.nih.gov/pubmed/25552858
http://dx.doi.org/10.4103/0976-3147.143208
work_keys_str_mv AT bampssven posterolateralapproachinaneurofibromatosistypeipatientwithseveredystrophicthoracickyphoscoliosisacasereportcadaverstudyandliteraturereview
AT calenberghfrankvan posterolateralapproachinaneurofibromatosistypeipatientwithseveredystrophicthoracickyphoscoliosisacasereportcadaverstudyandliteraturereview
AT loonjohanvan posterolateralapproachinaneurofibromatosistypeipatientwithseveredystrophicthoracickyphoscoliosisacasereportcadaverstudyandliteraturereview
AT paesschenrafvan posterolateralapproachinaneurofibromatosistypeipatientwithseveredystrophicthoracickyphoscoliosisacasereportcadaverstudyandliteraturereview
AT vanderschotpaul posterolateralapproachinaneurofibromatosistypeipatientwithseveredystrophicthoracickyphoscoliosisacasereportcadaverstudyandliteraturereview