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Transmission Characteristics of Variably Protease-Sensitive Prionopathy

Variably protease-sensitive prionopathy (VPSPr), a recently identified and seemingly sporadic human prion disease, is distinct from Creutzfeldt-Jakob disease (CJD) but shares features of Gerstmann-Sträussler-Scheinker disease (GSS). However, contrary to exclusively inherited GSS, no prion protein (P...

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Detalles Bibliográficos
Autores principales:	Notari, Silvio, Xiao, Xiangzhu, Espinosa, Juan Carlos, Cohen, Yvonne, Qing, Liuting, Aguilar-Calvo, Patricia, Kofskey, Diane, Cali, Ignazio, Cracco, Laura, Kong, Qingzhong, Torres, Juan Maria, Zou, Wenquan, Gambetti, Pierluigi
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Centers for Disease Control and Prevention 2014
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4257788/ https://www.ncbi.nlm.nih.gov/pubmed/25418590 http://dx.doi.org/10.3201/eid2012.140548

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