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Distribution of Heparan Sulfate Oligosaccharides in Murine Mucopolysaccharidosis Type IIIA

Heparan sulfate (HS) catabolism begins with endo-degradation of the polysaccharide to smaller HS oligosaccharides, followed by the sequential action of exo-enzymes to reduce these oligosaccharides to monosaccharides and inorganic sulfate. In mucopolysaccharidosis type IIIA (MPS IIIA) the exo-enzyme,...

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Detalles Bibliográficos
Autores principales:	Mason, Kerryn, Meikle, Peter, Hopwood, John, Fuller, Maria
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2014
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4279159/ https://www.ncbi.nlm.nih.gov/pubmed/25513953 http://dx.doi.org/10.3390/metabo4041088

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