Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?

Klippel-Trenaunay syndrome (KTS) is a cutaneous capillary malformation on a limb in association with soft tissue swelling with or without bony hypertrophy and atypical varicosity. The capillary malformation associated with KTS is port wine stain. Angiokeratoma circumscriptum naeviforme (ACN) is a co...

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Autores principales: Wankhade, Vaishali, Singh, Rajesh, Sadhwani, Venus, Kodate, Purnima, Disawal, Amit
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4290170/
https://www.ncbi.nlm.nih.gov/pubmed/25593797
http://dx.doi.org/10.4103/2229-5178.146180
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author Wankhade, Vaishali
Singh, Rajesh
Sadhwani, Venus
Kodate, Purnima
Disawal, Amit
author_facet Wankhade, Vaishali
Singh, Rajesh
Sadhwani, Venus
Kodate, Purnima
Disawal, Amit
author_sort Wankhade, Vaishali
collection PubMed
description Klippel-Trenaunay syndrome (KTS) is a cutaneous capillary malformation on a limb in association with soft tissue swelling with or without bony hypertrophy and atypical varicosity. The capillary malformation associated with KTS is port wine stain. Angiokeratoma circumscriptum naeviforme (ACN) is a congenital variant of angiokeratoma commonly present on the lower limb as a hyperkeratotic plaque. ACN is rarely associated with KTS. We report a case of ACN with soft tissue hypertrophy and deep venous malformation (possibly a variant of Klippel-Trenaunay) in a 4-year-old male child.
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spelling pubmed-42901702015-01-15 Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome? Wankhade, Vaishali Singh, Rajesh Sadhwani, Venus Kodate, Purnima Disawal, Amit Indian Dermatol Online J Case Report Klippel-Trenaunay syndrome (KTS) is a cutaneous capillary malformation on a limb in association with soft tissue swelling with or without bony hypertrophy and atypical varicosity. The capillary malformation associated with KTS is port wine stain. Angiokeratoma circumscriptum naeviforme (ACN) is a congenital variant of angiokeratoma commonly present on the lower limb as a hyperkeratotic plaque. ACN is rarely associated with KTS. We report a case of ACN with soft tissue hypertrophy and deep venous malformation (possibly a variant of Klippel-Trenaunay) in a 4-year-old male child. Medknow Publications & Media Pvt Ltd 2014-12 /pmc/articles/PMC4290170/ /pubmed/25593797 http://dx.doi.org/10.4103/2229-5178.146180 Text en Copyright: © Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Wankhade, Vaishali
Singh, Rajesh
Sadhwani, Venus
Kodate, Purnima
Disawal, Amit
Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?
title Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?
title_full Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?
title_fullStr Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?
title_full_unstemmed Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?
title_short Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?
title_sort angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: a variant of klippel-trenaunay syndrome?
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4290170/
https://www.ncbi.nlm.nih.gov/pubmed/25593797
http://dx.doi.org/10.4103/2229-5178.146180
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