Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy

Primary splenic angiosarcoma is an extremely rare and aggressive neoplasm of the vasculature. Uniformly, primary splenic angiosarcoma is a fatal disease despite early diagnosis and treatment. Only patients with localized disease amenable to surgical resection achieve long-term, disease-free survival...

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Autores principales: Serrano, Oscar K, Knapp, Esther, Huang, Kevin, Baran, Galina, Statter, Mindy, McClain, Danielle, Gill, Jonathan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4295483/
https://www.ncbi.nlm.nih.gov/pubmed/25487642
http://dx.doi.org/10.1186/1477-7819-12-379
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author Serrano, Oscar K
Knapp, Esther
Huang, Kevin
Baran, Galina
Statter, Mindy
McClain, Danielle
Gill, Jonathan
author_facet Serrano, Oscar K
Knapp, Esther
Huang, Kevin
Baran, Galina
Statter, Mindy
McClain, Danielle
Gill, Jonathan
author_sort Serrano, Oscar K
collection PubMed
description Primary splenic angiosarcoma is an extremely rare and aggressive neoplasm of the vasculature. Uniformly, primary splenic angiosarcoma is a fatal disease despite early diagnosis and treatment. Only patients with localized disease amenable to surgical resection achieve long-term, disease-free survival. We present a review of the literature and report a case of a 3-year-old girl with metastatic primary splenic angiosarcoma who was offered aggressive surgical and medical treatment with curative intent despite her advanced presentation.
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spelling pubmed-42954832015-01-16 Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy Serrano, Oscar K Knapp, Esther Huang, Kevin Baran, Galina Statter, Mindy McClain, Danielle Gill, Jonathan World J Surg Oncol Case Report Primary splenic angiosarcoma is an extremely rare and aggressive neoplasm of the vasculature. Uniformly, primary splenic angiosarcoma is a fatal disease despite early diagnosis and treatment. Only patients with localized disease amenable to surgical resection achieve long-term, disease-free survival. We present a review of the literature and report a case of a 3-year-old girl with metastatic primary splenic angiosarcoma who was offered aggressive surgical and medical treatment with curative intent despite her advanced presentation. BioMed Central 2014-12-09 /pmc/articles/PMC4295483/ /pubmed/25487642 http://dx.doi.org/10.1186/1477-7819-12-379 Text en © Serrano et al.; licensee BioMed Central Ltd. 2014 This article is published under license to BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly credited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Serrano, Oscar K
Knapp, Esther
Huang, Kevin
Baran, Galina
Statter, Mindy
McClain, Danielle
Gill, Jonathan
Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy
title Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy
title_full Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy
title_fullStr Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy
title_full_unstemmed Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy
title_short Pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy
title_sort pediatric primary splenic angiosarcoma: an aggressive multidisciplinary approach to the oncologic management of a rare malignancy
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4295483/
https://www.ncbi.nlm.nih.gov/pubmed/25487642
http://dx.doi.org/10.1186/1477-7819-12-379
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