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Glycogen storage disease type III: modified Atkins diet improves myopathy

BACKGROUND: Frequent feeds with carbohydrate-rich meals or continuous enteral feeding has been the therapy of choice in glycogen storage disease (Glycogenosis) type III. Recent guidelines on diagnosis and management recommend frequent feedings with high complex carbohydrates or cornstarch avoiding f...

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Detalles Bibliográficos
Autores principales:	Mayorandan, Sebene, Meyer, Uta, Hartmann, Hans, Das, Anibh Martin
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2014
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4302571/ https://www.ncbi.nlm.nih.gov/pubmed/25431232 http://dx.doi.org/10.1186/s13023-014-0196-3

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