A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement

Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the e...

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Autores principales: Kim, Bong Jun, Kim, Tae Hoon, Kim, Do Jung, Noh, Dongsub, Ham, Seok Jin, Lee, Sungsoo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Society for Thoracic and Cardiovascular Surgery 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4333852/
https://www.ncbi.nlm.nih.gov/pubmed/25705608
http://dx.doi.org/10.5090/kjtcs.2015.48.1.90
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author Kim, Bong Jun
Kim, Tae Hoon
Kim, Do Jung
Noh, Dongsub
Ham, Seok Jin
Lee, Sungsoo
author_facet Kim, Bong Jun
Kim, Tae Hoon
Kim, Do Jung
Noh, Dongsub
Ham, Seok Jin
Lee, Sungsoo
author_sort Kim, Bong Jun
collection PubMed
description Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.
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spelling pubmed-43338522015-02-20 A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement Kim, Bong Jun Kim, Tae Hoon Kim, Do Jung Noh, Dongsub Ham, Seok Jin Lee, Sungsoo Korean J Thorac Cardiovasc Surg Case Report Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs. The Korean Society for Thoracic and Cardiovascular Surgery 2015-02 2015-02-05 /pmc/articles/PMC4333852/ /pubmed/25705608 http://dx.doi.org/10.5090/kjtcs.2015.48.1.90 Text en Copyright © 2015 by The Korean Society for Thoracic and Cardiovascular Surgery. All rights Reserved. This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Kim, Bong Jun
Kim, Tae Hoon
Kim, Do Jung
Noh, Dongsub
Ham, Seok Jin
Lee, Sungsoo
A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
title A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
title_full A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
title_fullStr A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
title_full_unstemmed A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
title_short A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
title_sort successfully treated case of gorham-stout syndrome with sternal involvement
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4333852/
https://www.ncbi.nlm.nih.gov/pubmed/25705608
http://dx.doi.org/10.5090/kjtcs.2015.48.1.90
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