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Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case
Loeys–Dietz syndrome (LDS) is a recognized connective tissue disorder characterized by progressive aortic aneurysm and dissection. Patients are at high risk of aortic dissection or rupture at an early age, but to our knowledge, surgery on the great arteries has never been attempted in the neonatal p...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Springer Japan
2014
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4359291/ https://www.ncbi.nlm.nih.gov/pubmed/24817126 http://dx.doi.org/10.1007/s00595-014-0910-8 |
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author | Ozawa, Hideto Kawata, Hiroaki Iwai, Shigemitsu Yamauchi, Sanae Kanaya, Tomomitsu Kishimoto, Hidefumi |
author_facet | Ozawa, Hideto Kawata, Hiroaki Iwai, Shigemitsu Yamauchi, Sanae Kanaya, Tomomitsu Kishimoto, Hidefumi |
author_sort | Ozawa, Hideto |
collection | PubMed |
description | Loeys–Dietz syndrome (LDS) is a recognized connective tissue disorder characterized by progressive aortic aneurysm and dissection. Patients are at high risk of aortic dissection or rupture at an early age, but to our knowledge, surgery on the great arteries has never been attempted in the neonatal period. We report a case of LDS with dilated pulmonary arteries and an interrupted aortic arch complex in a neonate. We performed bilateral pulmonary artery banding, but 12 days after the procedure, the infant died of rupture of the distal portion of the banding sites following massive dilatation. |
format | Online Article Text |
id | pubmed-4359291 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Springer Japan |
record_format | MEDLINE/PubMed |
spelling | pubmed-43592912015-03-18 Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case Ozawa, Hideto Kawata, Hiroaki Iwai, Shigemitsu Yamauchi, Sanae Kanaya, Tomomitsu Kishimoto, Hidefumi Surg Today Case Report Loeys–Dietz syndrome (LDS) is a recognized connective tissue disorder characterized by progressive aortic aneurysm and dissection. Patients are at high risk of aortic dissection or rupture at an early age, but to our knowledge, surgery on the great arteries has never been attempted in the neonatal period. We report a case of LDS with dilated pulmonary arteries and an interrupted aortic arch complex in a neonate. We performed bilateral pulmonary artery banding, but 12 days after the procedure, the infant died of rupture of the distal portion of the banding sites following massive dilatation. Springer Japan 2014-05-11 2015 /pmc/articles/PMC4359291/ /pubmed/24817126 http://dx.doi.org/10.1007/s00595-014-0910-8 Text en © The Author(s) 2014 https://creativecommons.org/licenses/by/4.0/ Open AccessThis article is distributed under the terms of the Creative Commons Attribution License which permits any use, distribution, and reproduction in any medium, provided the original author(s) and the source are credited. |
spellingShingle | Case Report Ozawa, Hideto Kawata, Hiroaki Iwai, Shigemitsu Yamauchi, Sanae Kanaya, Tomomitsu Kishimoto, Hidefumi Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case |
title | Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case |
title_full | Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case |
title_fullStr | Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case |
title_full_unstemmed | Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case |
title_short | Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case |
title_sort | pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with loeys–dietz syndrome and an interrupted aortic arch complex: report of a case |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4359291/ https://www.ncbi.nlm.nih.gov/pubmed/24817126 http://dx.doi.org/10.1007/s00595-014-0910-8 |
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