Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case

Loeys–Dietz syndrome (LDS) is a recognized connective tissue disorder characterized by progressive aortic aneurysm and dissection. Patients are at high risk of aortic dissection or rupture at an early age, but to our knowledge, surgery on the great arteries has never been attempted in the neonatal p...

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Autores principales: Ozawa, Hideto, Kawata, Hiroaki, Iwai, Shigemitsu, Yamauchi, Sanae, Kanaya, Tomomitsu, Kishimoto, Hidefumi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer Japan 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4359291/
https://www.ncbi.nlm.nih.gov/pubmed/24817126
http://dx.doi.org/10.1007/s00595-014-0910-8
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author Ozawa, Hideto
Kawata, Hiroaki
Iwai, Shigemitsu
Yamauchi, Sanae
Kanaya, Tomomitsu
Kishimoto, Hidefumi
author_facet Ozawa, Hideto
Kawata, Hiroaki
Iwai, Shigemitsu
Yamauchi, Sanae
Kanaya, Tomomitsu
Kishimoto, Hidefumi
author_sort Ozawa, Hideto
collection PubMed
description Loeys–Dietz syndrome (LDS) is a recognized connective tissue disorder characterized by progressive aortic aneurysm and dissection. Patients are at high risk of aortic dissection or rupture at an early age, but to our knowledge, surgery on the great arteries has never been attempted in the neonatal period. We report a case of LDS with dilated pulmonary arteries and an interrupted aortic arch complex in a neonate. We performed bilateral pulmonary artery banding, but 12 days after the procedure, the infant died of rupture of the distal portion of the banding sites following massive dilatation.
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spelling pubmed-43592912015-03-18 Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case Ozawa, Hideto Kawata, Hiroaki Iwai, Shigemitsu Yamauchi, Sanae Kanaya, Tomomitsu Kishimoto, Hidefumi Surg Today Case Report Loeys–Dietz syndrome (LDS) is a recognized connective tissue disorder characterized by progressive aortic aneurysm and dissection. Patients are at high risk of aortic dissection or rupture at an early age, but to our knowledge, surgery on the great arteries has never been attempted in the neonatal period. We report a case of LDS with dilated pulmonary arteries and an interrupted aortic arch complex in a neonate. We performed bilateral pulmonary artery banding, but 12 days after the procedure, the infant died of rupture of the distal portion of the banding sites following massive dilatation. Springer Japan 2014-05-11 2015 /pmc/articles/PMC4359291/ /pubmed/24817126 http://dx.doi.org/10.1007/s00595-014-0910-8 Text en © The Author(s) 2014 https://creativecommons.org/licenses/by/4.0/ Open AccessThis article is distributed under the terms of the Creative Commons Attribution License which permits any use, distribution, and reproduction in any medium, provided the original author(s) and the source are credited.
spellingShingle Case Report
Ozawa, Hideto
Kawata, Hiroaki
Iwai, Shigemitsu
Yamauchi, Sanae
Kanaya, Tomomitsu
Kishimoto, Hidefumi
Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case
title Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case
title_full Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case
title_fullStr Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case
title_full_unstemmed Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case
title_short Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys–Dietz syndrome and an interrupted aortic arch complex: report of a case
title_sort pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with loeys–dietz syndrome and an interrupted aortic arch complex: report of a case
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4359291/
https://www.ncbi.nlm.nih.gov/pubmed/24817126
http://dx.doi.org/10.1007/s00595-014-0910-8
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