A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra

Bilateral cystic nephroma is an extremely rare benign renal neoplasm. Here we present a case of bilateral cystic nephroma in a four month old boy who subsequently developed embryonal rhabdomyosarcoma of the urethra. Both tumors were successfully treated. To our knowledge this is the first reported c...

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Autores principales: Kurian, Jujju Jacob, Sen, Sudipta, Joseph, Reju Thomas, Bindra, Mandeep Singh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4360460/
https://www.ncbi.nlm.nih.gov/pubmed/25829672
http://dx.doi.org/10.4103/0971-9261.151553
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author Kurian, Jujju Jacob
Sen, Sudipta
Joseph, Reju Thomas
Bindra, Mandeep Singh
author_facet Kurian, Jujju Jacob
Sen, Sudipta
Joseph, Reju Thomas
Bindra, Mandeep Singh
author_sort Kurian, Jujju Jacob
collection PubMed
description Bilateral cystic nephroma is an extremely rare benign renal neoplasm. Here we present a case of bilateral cystic nephroma in a four month old boy who subsequently developed embryonal rhabdomyosarcoma of the urethra. Both tumors were successfully treated. To our knowledge this is the first reported case of this association which could be related to Dicer-1 mutation.
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spelling pubmed-43604602015-04-01 A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra Kurian, Jujju Jacob Sen, Sudipta Joseph, Reju Thomas Bindra, Mandeep Singh J Indian Assoc Pediatr Surg Case Report Bilateral cystic nephroma is an extremely rare benign renal neoplasm. Here we present a case of bilateral cystic nephroma in a four month old boy who subsequently developed embryonal rhabdomyosarcoma of the urethra. Both tumors were successfully treated. To our knowledge this is the first reported case of this association which could be related to Dicer-1 mutation. Medknow Publications & Media Pvt Ltd 2015 /pmc/articles/PMC4360460/ /pubmed/25829672 http://dx.doi.org/10.4103/0971-9261.151553 Text en Copyright: © Journal of Indian Association of Pediatric Surgeons http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Kurian, Jujju Jacob
Sen, Sudipta
Joseph, Reju Thomas
Bindra, Mandeep Singh
A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
title A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
title_full A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
title_fullStr A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
title_full_unstemmed A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
title_short A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
title_sort rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4360460/
https://www.ncbi.nlm.nih.gov/pubmed/25829672
http://dx.doi.org/10.4103/0971-9261.151553
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