Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony

Progressive hemifacial atrophy (PHA) is a disease of unknown etiology affecting one-half of the face. Ocular involvement is uncommon. Atrophy of iris is rare, with only a few cases of partial atrophy being reported in the literature. We report a case of total atrophy of iris and ciliary body with as...

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Autores principales: Kini, T Ashwini, Prakash, V S, Puthalath, Suresh, Bhandari, P L
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2015
Materias:
Brief Communications
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4363961/
https://www.ncbi.nlm.nih.gov/pubmed/25686066
http://dx.doi.org/10.4103/0301-4738.151474
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author Kini, T Ashwini
Prakash, V S
Puthalath, Suresh
Bhandari, P L
author_facet Kini, T Ashwini
Prakash, V S
Puthalath, Suresh
Bhandari, P L
author_sort Kini, T Ashwini
collection PubMed
description Progressive hemifacial atrophy (PHA) is a disease of unknown etiology affecting one-half of the face. Ocular involvement is uncommon. Atrophy of iris is rare, with only a few cases of partial atrophy being reported in the literature. We report a case of total atrophy of iris and ciliary body with associated ocular hypotony in a 16-year-old girl with PHA. We believe this is the first reported case of complete atrophy of iris and ciliary body in PHA. Ocular hypotony in PHA was thought to be due to intra-ocular inflammation. However in our case it appears to be secondary to severe atrophy of the ciliary body.
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spelling pubmed-43639612015-03-25 Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony Kini, T Ashwini Prakash, V S Puthalath, Suresh Bhandari, P L Indian J Ophthalmol Brief Communications Progressive hemifacial atrophy (PHA) is a disease of unknown etiology affecting one-half of the face. Ocular involvement is uncommon. Atrophy of iris is rare, with only a few cases of partial atrophy being reported in the literature. We report a case of total atrophy of iris and ciliary body with associated ocular hypotony in a 16-year-old girl with PHA. We believe this is the first reported case of complete atrophy of iris and ciliary body in PHA. Ocular hypotony in PHA was thought to be due to intra-ocular inflammation. However in our case it appears to be secondary to severe atrophy of the ciliary body. Medknow Publications & Media Pvt Ltd 2015-01 /pmc/articles/PMC4363961/ /pubmed/25686066 http://dx.doi.org/10.4103/0301-4738.151474 Text en Copyright: © Indian Journal of Ophthalmology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Brief Communications
Kini, T Ashwini
Prakash, V S
Puthalath, Suresh
Bhandari, P L
Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony
title Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony
title_full Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony
title_fullStr Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony
title_full_unstemmed Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony
title_short Progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony
title_sort progressive hemifacial atrophy with ciliary body atrophy and ocular hypotony
topic Brief Communications
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4363961/
https://www.ncbi.nlm.nih.gov/pubmed/25686066
http://dx.doi.org/10.4103/0301-4738.151474
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AT puthalathsuresh progressivehemifacialatrophywithciliarybodyatrophyandocularhypotony
AT bhandaripl progressivehemifacialatrophywithciliarybodyatrophyandocularhypotony

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