Malignant Rhabdoid Tumor of the Liver: A Case Report and Literature Review

Malignant rhabdoid tumor (MRT) is a rare and aggressive malignancy associated with poor outcomes. MRT of the liver is even rarer, and little information has been described. We report the case of an 8-month-old boy with MRT of the liver. The tumor showed aggressive progression despite a multidiscipli...

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Detalles Bibliográficos
Autores principales: Oita, Satoru, Terui, Keita, Komatsu, Syugo, Hishiki, Tomoro, Saito, Takeshi, Mitsunaga, Tetsuya, Nakata, Mitsuyuki, Yoshida, Hideo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: PAGEPress Publications, Pavia, Italy 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4387326/
https://www.ncbi.nlm.nih.gov/pubmed/25918621
http://dx.doi.org/10.4081/pr.2015.5578
Descripción
Sumario:Malignant rhabdoid tumor (MRT) is a rare and aggressive malignancy associated with poor outcomes. MRT of the liver is even rarer, and little information has been described. We report the case of an 8-month-old boy with MRT of the liver. The tumor showed aggressive progression despite a multidisciplinary approach, and the patient died due to multiple organ failure 14 days after admission. Autopsy revealed the liver tumor and multiple metastases with negative immunohistochemistry for INI1/BAF47. A review of 53 cases of pediatric MRT of the liver is provided.

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