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Metabolic Dysfunction and Altered Mitochondrial Dynamics in the Utrophin-Dystrophin Deficient Mouse Model of Duchenne Muscular Dystrophy

The utrophin-dystrophin deficient (DKO) mouse model has been widely used to understand the progression of Duchenne muscular dystrophy (DMD). However, it is unclear as to what extent muscle pathology affects metabolism. Therefore, the present study was focused on understanding energy expenditure in t...

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Detalles Bibliográficos
Autores principales:	Pant, Meghna, Sopariwala, Danesh H., Bal, Naresh C., Lowe, Jeovanna, Delfín, Dawn A., Rafael-Fortney, Jill, Periasamy, Muthu
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2015
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4393257/ https://www.ncbi.nlm.nih.gov/pubmed/25859846 http://dx.doi.org/10.1371/journal.pone.0123875

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