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Laser ablation inductively coupled plasma mass spectrometry imaging of metals in experimental and clinical Wilson's disease
Wilson's disease is an autosomal recessive disorder in which the liver does not properly release copper into bile, resulting in prominent copper accumulation in various tissues. Affected patients suffer from hepatic disorders and severe neurological defects. Experimental studies in mutant mice...
Autores principales: | Boaru, Sorina Georgiana, Merle, Uta, Uerlings, Ricarda, Zimmermann, Astrid, Flechtenmacher, Christa, Willheim, Claudia, Eder, Elisabeth, Ferenci, Peter, Stremmel, Wolfgang, Weiskirchen, Ralf |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BlackWell Publishing Ltd
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4395195/ https://www.ncbi.nlm.nih.gov/pubmed/25704483 http://dx.doi.org/10.1111/jcmm.12497 |
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