Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation

The syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in th...

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Autores principales: Ramji, Jaishri, Joshi, Rakesh S, Bachani, Mitesh, Rathore, Dungarsingh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: EL-MED-Pub 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4420296/
https://www.ncbi.nlm.nih.gov/pubmed/26023464
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author Ramji, Jaishri
Joshi, Rakesh S
Bachani, Mitesh
Rathore, Dungarsingh
author_facet Ramji, Jaishri
Joshi, Rakesh S
Bachani, Mitesh
Rathore, Dungarsingh
author_sort Ramji, Jaishri
collection PubMed
description The syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in the neonatal period. Inspite of successful Kasai’s portoenterostomy at 52nd day of life, the child succumbed to post-operative sepsis.
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spelling pubmed-44202962015-05-28 Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation Ramji, Jaishri Joshi, Rakesh S Bachani, Mitesh Rathore, Dungarsingh J Neonatal Surg Case Report The syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in the neonatal period. Inspite of successful Kasai’s portoenterostomy at 52nd day of life, the child succumbed to post-operative sepsis. EL-MED-Pub 2013-10-01 /pmc/articles/PMC4420296/ /pubmed/26023464 Text en Copyright © 2013 Ramji et al http://creativecommons.org/licenses/by/3.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Ramji, Jaishri
Joshi, Rakesh S
Bachani, Mitesh
Rathore, Dungarsingh
Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
title Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
title_full Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
title_fullStr Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
title_full_unstemmed Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
title_short Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
title_sort extra-hepatic biliary atresia in association with polysplenia and intestinal malrotation
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4420296/
https://www.ncbi.nlm.nih.gov/pubmed/26023464
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