A case of primary immune deficiency presenting with nephrotic syndrome

Common variable immunodeficiency (CVID) is the most common form of severe antibody deficiency. The disorder is associated with a broad spectrum of clinical manifestations, including infections and chronic lung, gastrointestinal and autoimmune diseases. A 29-year-old female patient has had frequent s...

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Autores principales: Aydin, Zeki, Gursu, Meltem, Ozturk, Savas, Kilicaslan, Isın, Kazancioglu, Rumeyza
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2010
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4421686/
https://www.ncbi.nlm.nih.gov/pubmed/25984052
http://dx.doi.org/10.1093/ndtplus/sfq083
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author Aydin, Zeki
Gursu, Meltem
Ozturk, Savas
Kilicaslan, Isın
Kazancioglu, Rumeyza
author_facet Aydin, Zeki
Gursu, Meltem
Ozturk, Savas
Kilicaslan, Isın
Kazancioglu, Rumeyza
author_sort Aydin, Zeki
collection PubMed
description Common variable immunodeficiency (CVID) is the most common form of severe antibody deficiency. The disorder is associated with a broad spectrum of clinical manifestations, including infections and chronic lung, gastrointestinal and autoimmune diseases. A 29-year-old female patient has had frequent sinopulmonary infections and gastroenteritis for the last 20 years and had been given broad-spectrum antibiotics for treatment. Immunoglobulin (Ig) levels were at undetectable levels. Renal biopsy was consistent with AA amyloidosis. She is now under follow-up with periodic intravenous Ig treatment without any infection during the last 10 months. CVID must be kept in mind in patients with recurrent sinopulmonary infections.
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spelling pubmed-44216862015-05-15 A case of primary immune deficiency presenting with nephrotic syndrome Aydin, Zeki Gursu, Meltem Ozturk, Savas Kilicaslan, Isın Kazancioglu, Rumeyza NDT Plus Case Report Common variable immunodeficiency (CVID) is the most common form of severe antibody deficiency. The disorder is associated with a broad spectrum of clinical manifestations, including infections and chronic lung, gastrointestinal and autoimmune diseases. A 29-year-old female patient has had frequent sinopulmonary infections and gastroenteritis for the last 20 years and had been given broad-spectrum antibiotics for treatment. Immunoglobulin (Ig) levels were at undetectable levels. Renal biopsy was consistent with AA amyloidosis. She is now under follow-up with periodic intravenous Ig treatment without any infection during the last 10 months. CVID must be kept in mind in patients with recurrent sinopulmonary infections. Oxford University Press 2010-10 2010-05-11 /pmc/articles/PMC4421686/ /pubmed/25984052 http://dx.doi.org/10.1093/ndtplus/sfq083 Text en © The Author 2010. Published by Oxford University Press on behalf of ERA-EDTA. All rights reserved. For permissions, please e-mail: journals.permissions@oxfordjournals.org http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
Aydin, Zeki
Gursu, Meltem
Ozturk, Savas
Kilicaslan, Isın
Kazancioglu, Rumeyza
A case of primary immune deficiency presenting with nephrotic syndrome
title A case of primary immune deficiency presenting with nephrotic syndrome
title_full A case of primary immune deficiency presenting with nephrotic syndrome
title_fullStr A case of primary immune deficiency presenting with nephrotic syndrome
title_full_unstemmed A case of primary immune deficiency presenting with nephrotic syndrome
title_short A case of primary immune deficiency presenting with nephrotic syndrome
title_sort case of primary immune deficiency presenting with nephrotic syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4421686/
https://www.ncbi.nlm.nih.gov/pubmed/25984052
http://dx.doi.org/10.1093/ndtplus/sfq083
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