Cargando…
Hydranencephaly: cerebral spinal fluid instead of cerebral mantles
The authors report a wide and updated revision of hydranencephaly, including a literature review, and present the case of a patient affected by this condition, still alive at 36 months. Hydranencephaly is an isolated and with a severe prognosis abnormality, affecting the cerebral mantle. In this con...
Autores principales: | , , , , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2014
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4421920/ https://www.ncbi.nlm.nih.gov/pubmed/25326191 http://dx.doi.org/10.1186/s13052-014-0079-1 |
_version_ | 1782369972918419456 |
---|---|
author | Pavone, Piero Praticò, Andrea D Vitaliti, Giovanna Ruggieri, Martino Rizzo, Renata Parano, Enrico Pavone, Lorenzo Pero, Giuseppe Falsaperla, Raffaele |
author_facet | Pavone, Piero Praticò, Andrea D Vitaliti, Giovanna Ruggieri, Martino Rizzo, Renata Parano, Enrico Pavone, Lorenzo Pero, Giuseppe Falsaperla, Raffaele |
author_sort | Pavone, Piero |
collection | PubMed |
description | The authors report a wide and updated revision of hydranencephaly, including a literature review, and present the case of a patient affected by this condition, still alive at 36 months. Hydranencephaly is an isolated and with a severe prognosis abnormality, affecting the cerebral mantle. In this condition, the cerebral hemispheres are completely or almost completely absent and are replaced by a membranous sac filled with cerebrospinal fluid. Midbrain is usually not involved. Hydranencephaly is a relatively rare cerebral disorder. Differential diagnosis is mainly relevant when considering severe hydrocephalus, poroencephalic cyst and alobar holoprosencephaly. Ethical questions related to the correct criteria for the surgical treatment are also discussed. |
format | Online Article Text |
id | pubmed-4421920 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | BioMed Central |
record_format | MEDLINE/PubMed |
spelling | pubmed-44219202015-05-07 Hydranencephaly: cerebral spinal fluid instead of cerebral mantles Pavone, Piero Praticò, Andrea D Vitaliti, Giovanna Ruggieri, Martino Rizzo, Renata Parano, Enrico Pavone, Lorenzo Pero, Giuseppe Falsaperla, Raffaele Ital J Pediatr Review The authors report a wide and updated revision of hydranencephaly, including a literature review, and present the case of a patient affected by this condition, still alive at 36 months. Hydranencephaly is an isolated and with a severe prognosis abnormality, affecting the cerebral mantle. In this condition, the cerebral hemispheres are completely or almost completely absent and are replaced by a membranous sac filled with cerebrospinal fluid. Midbrain is usually not involved. Hydranencephaly is a relatively rare cerebral disorder. Differential diagnosis is mainly relevant when considering severe hydrocephalus, poroencephalic cyst and alobar holoprosencephaly. Ethical questions related to the correct criteria for the surgical treatment are also discussed. BioMed Central 2014-10-18 /pmc/articles/PMC4421920/ /pubmed/25326191 http://dx.doi.org/10.1186/s13052-014-0079-1 Text en © Pavone et al.; licensee BioMed Central Ltd. 2014 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly credited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated. |
spellingShingle | Review Pavone, Piero Praticò, Andrea D Vitaliti, Giovanna Ruggieri, Martino Rizzo, Renata Parano, Enrico Pavone, Lorenzo Pero, Giuseppe Falsaperla, Raffaele Hydranencephaly: cerebral spinal fluid instead of cerebral mantles |
title | Hydranencephaly: cerebral spinal fluid instead of cerebral mantles |
title_full | Hydranencephaly: cerebral spinal fluid instead of cerebral mantles |
title_fullStr | Hydranencephaly: cerebral spinal fluid instead of cerebral mantles |
title_full_unstemmed | Hydranencephaly: cerebral spinal fluid instead of cerebral mantles |
title_short | Hydranencephaly: cerebral spinal fluid instead of cerebral mantles |
title_sort | hydranencephaly: cerebral spinal fluid instead of cerebral mantles |
topic | Review |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4421920/ https://www.ncbi.nlm.nih.gov/pubmed/25326191 http://dx.doi.org/10.1186/s13052-014-0079-1 |
work_keys_str_mv | AT pavonepiero hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT praticoandread hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT vitalitigiovanna hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT ruggierimartino hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT rizzorenata hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT paranoenrico hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT pavonelorenzo hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT perogiuseppe hydranencephalycerebralspinalfluidinsteadofcerebralmantles AT falsaperlaraffaele hydranencephalycerebralspinalfluidinsteadofcerebralmantles |