Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique

Rhabdomyosarcoma (RMS) is the most common sarcoma in paediatric patients. A perianal site is unusual and is associated with a low cure rate. The few cases of reported perianal RMS have been associated with sequelae. Here, we report the case of a 29-month-old male child who received sequential treatm...

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Autores principales: Demoor-Goldschmidt, Charlotte, Dumoucel, Sophie, Haie-Meder, Christine, Corradini, Nadège, Mahé, Marc-André, Supiot, Stéphane
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4422314/
https://www.ncbi.nlm.nih.gov/pubmed/25927819
http://dx.doi.org/10.1186/s13014-015-0413-9
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author Demoor-Goldschmidt, Charlotte
Dumoucel, Sophie
Haie-Meder, Christine
Corradini, Nadège
Mahé, Marc-André
Supiot, Stéphane
author_facet Demoor-Goldschmidt, Charlotte
Dumoucel, Sophie
Haie-Meder, Christine
Corradini, Nadège
Mahé, Marc-André
Supiot, Stéphane
author_sort Demoor-Goldschmidt, Charlotte
collection PubMed
description Rhabdomyosarcoma (RMS) is the most common sarcoma in paediatric patients. A perianal site is unusual and is associated with a low cure rate. The few cases of reported perianal RMS have been associated with sequelae. Here, we report the case of a 29-month-old male child who received sequential treatment by surgery, chemotherapy and radiotherapy inspired by Papillon’s irradiation of adult anal/low-rectum cancers (including external beam radiotherapy in the gynecological exam position followed by brachytherapy) and who remains in complete remission 49 months post treatment with no sphincter or other anorectal disorders.
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spelling pubmed-44223142015-05-07 Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique Demoor-Goldschmidt, Charlotte Dumoucel, Sophie Haie-Meder, Christine Corradini, Nadège Mahé, Marc-André Supiot, Stéphane Radiat Oncol Case Report Rhabdomyosarcoma (RMS) is the most common sarcoma in paediatric patients. A perianal site is unusual and is associated with a low cure rate. The few cases of reported perianal RMS have been associated with sequelae. Here, we report the case of a 29-month-old male child who received sequential treatment by surgery, chemotherapy and radiotherapy inspired by Papillon’s irradiation of adult anal/low-rectum cancers (including external beam radiotherapy in the gynecological exam position followed by brachytherapy) and who remains in complete remission 49 months post treatment with no sphincter or other anorectal disorders. BioMed Central 2015-05-01 /pmc/articles/PMC4422314/ /pubmed/25927819 http://dx.doi.org/10.1186/s13014-015-0413-9 Text en © Demoor-Goldschmidt et al.; licensee BioMed Central. 2015 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly credited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Demoor-Goldschmidt, Charlotte
Dumoucel, Sophie
Haie-Meder, Christine
Corradini, Nadège
Mahé, Marc-André
Supiot, Stéphane
Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique
title Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique
title_full Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique
title_fullStr Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique
title_full_unstemmed Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique
title_short Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique
title_sort conservative management of a perianal rhabdomyosarcoma in a 2-year old child by papillon’s technique
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4422314/
https://www.ncbi.nlm.nih.gov/pubmed/25927819
http://dx.doi.org/10.1186/s13014-015-0413-9
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