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Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation

Introduction: Few cases of cochlear implantation (CI) in neurofibromatosis type 2 (NF2) patients had been reported in the literature. The approaches described were translabyrinthine, retrosigmoid or middle cranial fossa. Objectives: To describe a case of a NF2- deafened-patient who underwent to vest...

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Autores principales: Bento, Ricardo Ferreira, Monteiro, Tatiana Alves, Bittencourt, Aline Gomes, Goffi-Gomez, Maria Valeria Schmidt, de Brito, Rubens
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Thieme Publicações Ltda 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4423271/
https://www.ncbi.nlm.nih.gov/pubmed/25992034
http://dx.doi.org/10.7162/S1809-977720130003000018
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author Bento, Ricardo Ferreira
Monteiro, Tatiana Alves
Bittencourt, Aline Gomes
Goffi-Gomez, Maria Valeria Schmidt
de Brito, Rubens
author_facet Bento, Ricardo Ferreira
Monteiro, Tatiana Alves
Bittencourt, Aline Gomes
Goffi-Gomez, Maria Valeria Schmidt
de Brito, Rubens
author_sort Bento, Ricardo Ferreira
collection PubMed
description Introduction: Few cases of cochlear implantation (CI) in neurofibromatosis type 2 (NF2) patients had been reported in the literature. The approaches described were translabyrinthine, retrosigmoid or middle cranial fossa. Objectives: To describe a case of a NF2- deafened-patient who underwent to vestibular schwannoma resection via RLA with cochlear nerve preservation and CI through the round window, at the same surgical time. Resumed Report: A 36-year-old woman with severe bilateral hearing loss due to NF2 was submitted to vestibular schwannoma resection and simultaneous CI. Functional assessment of cochlear nerve was performed by electrical promontory stimulation. Complete tumor removal was accomplishment via RLA with anatomic and functional cochlear and facial nerve preservation. Cochlear electrode array was partially inserted via round window. Sound field hearing threshold improvement was achieved. Mean tonal threshold was 46.2 dB HL. The patient could only detect environmental sounds and human voice but cannot discriminate vowels, words nor do sentences at 2 years of follow-up. Conclusion: Cochlear implantation is a feasible auditory restoration option in NF2 when cochlear anatomic and functional nerve preservation is achieved. The RLA is adequate for this purpose and features as an option for hearing preservation in NF2 patients.
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spelling pubmed-44232712015-05-19 Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation Bento, Ricardo Ferreira Monteiro, Tatiana Alves Bittencourt, Aline Gomes Goffi-Gomez, Maria Valeria Schmidt de Brito, Rubens Int Arch Otorhinolaryngol Article Introduction: Few cases of cochlear implantation (CI) in neurofibromatosis type 2 (NF2) patients had been reported in the literature. The approaches described were translabyrinthine, retrosigmoid or middle cranial fossa. Objectives: To describe a case of a NF2- deafened-patient who underwent to vestibular schwannoma resection via RLA with cochlear nerve preservation and CI through the round window, at the same surgical time. Resumed Report: A 36-year-old woman with severe bilateral hearing loss due to NF2 was submitted to vestibular schwannoma resection and simultaneous CI. Functional assessment of cochlear nerve was performed by electrical promontory stimulation. Complete tumor removal was accomplishment via RLA with anatomic and functional cochlear and facial nerve preservation. Cochlear electrode array was partially inserted via round window. Sound field hearing threshold improvement was achieved. Mean tonal threshold was 46.2 dB HL. The patient could only detect environmental sounds and human voice but cannot discriminate vowels, words nor do sentences at 2 years of follow-up. Conclusion: Cochlear implantation is a feasible auditory restoration option in NF2 when cochlear anatomic and functional nerve preservation is achieved. The RLA is adequate for this purpose and features as an option for hearing preservation in NF2 patients. Thieme Publicações Ltda 2013-07 /pmc/articles/PMC4423271/ /pubmed/25992034 http://dx.doi.org/10.7162/S1809-977720130003000018 Text en © Thieme Medical Publishers
spellingShingle Article
Bento, Ricardo Ferreira
Monteiro, Tatiana Alves
Bittencourt, Aline Gomes
Goffi-Gomez, Maria Valeria Schmidt
de Brito, Rubens
Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation
title Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation
title_full Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation
title_fullStr Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation
title_full_unstemmed Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation
title_short Retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation
title_sort retrolabyrinthine approach for cochlear nerve preservation in neurofibromatosis type 2 and simultaneous cochlear implantation
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4423271/
https://www.ncbi.nlm.nih.gov/pubmed/25992034
http://dx.doi.org/10.7162/S1809-977720130003000018
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