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Lung MRI and impairment of diaphragmatic function in Pompe disease

BACKGROUND: Pompe disease is a progressive metabolic myopathy. Involvement of respiratory muscles leads to progressive pulmonary dysfunction, particularly in supine position. Diaphragmatic weakness is considered to be the most important component. Standard spirometry is to some extent indicative but...

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Detalles Bibliográficos
Autores principales:	Wens, Stephan CA, Ciet, Pierluigi, Perez-Rovira, Adria, Logie, Karla, Salamon, Elizabeth, Wielopolski, Piotr, de Bruijne, Marleen, Kruijshaar, Michelle E, Tiddens, Harm AWM, van Doorn, Pieter A, van der Ploeg, Ans T
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2015
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4428089/ https://www.ncbi.nlm.nih.gov/pubmed/25943437 http://dx.doi.org/10.1186/s12890-015-0058-3

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