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Lipids in hepatic glycogen storage diseases: pathophysiology, monitoring of dietary management and future directions

Hepatic glycogen storage diseases (GSD) underscore the intimate relationship between carbohydrate and lipid metabolism. The hyperlipidemias in hepatic GSD reflect perturbed intracellular metabolism, providing biomarkers in blood to monitor dietary management. In different types of GSD, hyperlipidemi...

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Detalles Bibliográficos
Autores principales:	Derks, Terry G. J., van Rijn, Margreet
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Springer Netherlands 2015
Materias:	Glycogenoses
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4432100/ https://www.ncbi.nlm.nih.gov/pubmed/25633903 http://dx.doi.org/10.1007/s10545-015-9811-2

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