Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management

Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplanta...

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Autores principales: Singh, Anshuman, Pandey, VK, Tandon, Manish, Pandey, CK
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4445154/
https://www.ncbi.nlm.nih.gov/pubmed/26019357
http://dx.doi.org/10.4103/0019-5049.156888
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author Singh, Anshuman
Pandey, VK
Tandon, Manish
Pandey, CK
author_facet Singh, Anshuman
Pandey, VK
Tandon, Manish
Pandey, CK
author_sort Singh, Anshuman
collection PubMed
description Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplantation.
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spelling pubmed-44451542015-05-27 Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management Singh, Anshuman Pandey, VK Tandon, Manish Pandey, CK Indian J Anaesth Case Report Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplantation. Medknow Publications & Media Pvt Ltd 2015-05 /pmc/articles/PMC4445154/ /pubmed/26019357 http://dx.doi.org/10.4103/0019-5049.156888 Text en Copyright: © Indian Journal of Anaesthesia http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Singh, Anshuman
Pandey, VK
Tandon, Manish
Pandey, CK
Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
title Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
title_full Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
title_fullStr Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
title_full_unstemmed Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
title_short Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
title_sort dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4445154/
https://www.ncbi.nlm.nih.gov/pubmed/26019357
http://dx.doi.org/10.4103/0019-5049.156888
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