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Expression of Muscle-Specific MiRNA 206 in the Progression of Disease in a Murine SMA Model
Spinal muscular atrophy (SMA) is a severe neuromuscular disease, the most common in infancy, and the third one among young people under 18 years. The major pathological landmark of SMA is a selective degeneration of lower motor neurons, resulting in progressive skeletal muscle denervation, atrophy,...
Autores principales: | Valsecchi, Valeria, Boido, Marina, De Amicis, Elena, Piras, Antonio, Vercelli, Alessandro |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4450876/ https://www.ncbi.nlm.nih.gov/pubmed/26030275 http://dx.doi.org/10.1371/journal.pone.0128560 |
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