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Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis
Intravenous leiomyomatosis (IVL) is a rare neoplasm characterized by histologically benign-looking smooth muscle cell tumor mass, which is growing within the intrauterine and extrauterine venous system. In this report we aimed to present an unusual case of IVL, which is originating from iliac vein a...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi Publishing Corporation
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4465713/ https://www.ncbi.nlm.nih.gov/pubmed/26114006 http://dx.doi.org/10.1155/2015/658728 |
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author | Doganci, Suat Kaya, Erkan Kadan, Murat Karabacak, Kubilay Erol, Gökhan Demirkilic, Ufuk |
author_facet | Doganci, Suat Kaya, Erkan Kadan, Murat Karabacak, Kubilay Erol, Gökhan Demirkilic, Ufuk |
author_sort | Doganci, Suat |
collection | PubMed |
description | Intravenous leiomyomatosis (IVL) is a rare neoplasm characterized by histologically benign-looking smooth muscle cell tumor mass, which is growing within the intrauterine and extrauterine venous system. In this report we aimed to present an unusual case of IVL, which is originating from iliac vein and extended throughout to right cardiac chambers. A 49-year-old female patient, who was treated with warfarin sodium due to right iliac vein thrombosis, was admitted to our department with intermittent dyspnea, palpitation, and dizziness. Physical examination was almost normal except bilateral pretibial edema. On magnetic resonance venography, there was an intravenous mass, which is originated from right internal iliac vein and extended into the inferior vena cava. Transthoracic echocardiography and transesophageal echocardiography revealed a huge mass extending from the inferior vena cava through the right atrium, with obvious venous occlusion. Thoracic, abdominal, and pelvic MR showed an intravascular mass, which is concordant with leiomyomatosis. Surgery was performed through median sternotomy. A huge mass with 25-cm length and 186-gr weight was excised through right atrial oblique incision, on beating heart with cardiopulmonary bypass. Histopathologic assessment was compatible with IVL. Exact strategy for the surgical treatment of IVL is still controversial. We used one-stage approach, with complete resection of a huge IVL extending from right atrium to right iliac vein. In such cases, high recurrence rate is a significant problem; therefore it should be kept in mind. |
format | Online Article Text |
id | pubmed-4465713 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2015 |
publisher | Hindawi Publishing Corporation |
record_format | MEDLINE/PubMed |
spelling | pubmed-44657132015-06-25 Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis Doganci, Suat Kaya, Erkan Kadan, Murat Karabacak, Kubilay Erol, Gökhan Demirkilic, Ufuk Case Rep Surg Case Report Intravenous leiomyomatosis (IVL) is a rare neoplasm characterized by histologically benign-looking smooth muscle cell tumor mass, which is growing within the intrauterine and extrauterine venous system. In this report we aimed to present an unusual case of IVL, which is originating from iliac vein and extended throughout to right cardiac chambers. A 49-year-old female patient, who was treated with warfarin sodium due to right iliac vein thrombosis, was admitted to our department with intermittent dyspnea, palpitation, and dizziness. Physical examination was almost normal except bilateral pretibial edema. On magnetic resonance venography, there was an intravenous mass, which is originated from right internal iliac vein and extended into the inferior vena cava. Transthoracic echocardiography and transesophageal echocardiography revealed a huge mass extending from the inferior vena cava through the right atrium, with obvious venous occlusion. Thoracic, abdominal, and pelvic MR showed an intravascular mass, which is concordant with leiomyomatosis. Surgery was performed through median sternotomy. A huge mass with 25-cm length and 186-gr weight was excised through right atrial oblique incision, on beating heart with cardiopulmonary bypass. Histopathologic assessment was compatible with IVL. Exact strategy for the surgical treatment of IVL is still controversial. We used one-stage approach, with complete resection of a huge IVL extending from right atrium to right iliac vein. In such cases, high recurrence rate is a significant problem; therefore it should be kept in mind. Hindawi Publishing Corporation 2015 2015-05-31 /pmc/articles/PMC4465713/ /pubmed/26114006 http://dx.doi.org/10.1155/2015/658728 Text en Copyright © 2015 Suat Doganci et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Doganci, Suat Kaya, Erkan Kadan, Murat Karabacak, Kubilay Erol, Gökhan Demirkilic, Ufuk Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis |
title | Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis |
title_full | Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis |
title_fullStr | Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis |
title_full_unstemmed | Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis |
title_short | Huge Intravascular Tumor Extending to the Heart: Leiomyomatosis |
title_sort | huge intravascular tumor extending to the heart: leiomyomatosis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4465713/ https://www.ncbi.nlm.nih.gov/pubmed/26114006 http://dx.doi.org/10.1155/2015/658728 |
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