EEG–EMG polygraphic study of dystonia and myoclonus in a case of Creutzfeldt–Jakob disease()

We report on a patient with sporadic Creutzfeldt–Jakob disease (CJD) who showed dystonia, periodic myoclonus, and periodic sharp wave complexes (PSWCs) on EEG. The EEG–EMG polygraphic study revealed that dystonia appeared without relation to periodic myoclonus and PSWCs and that dystonia EMGs were s...

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Detalles Bibliográficos
Autores principales: Hashimoto, Takao, Iwahashi, Teruaki, Ishii, Wataru, Yamamoto, Kanji, Ikeda, Shu-ichi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4485673/
https://www.ncbi.nlm.nih.gov/pubmed/26150924
http://dx.doi.org/10.1016/j.ebcr.2015.05.002
Descripción
Sumario:We report on a patient with sporadic Creutzfeldt–Jakob disease (CJD) who showed dystonia, periodic myoclonus, and periodic sharp wave complexes (PSWCs) on EEG. The EEG–EMG polygraphic study revealed that dystonia appeared without relation to periodic myoclonus and PSWCs and that dystonia EMGs were strongly suppressed after periodic myoclonus EMGs. These findings suggest that dystonia has a pathogenesis different from that of periodic myoclonus and PSWCs, but dystonia and periodic myoclonus may be generated through the sensorimotor cortex in CJD.

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