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Chronic myelomonocytic leukemia as a cause of fatal uncontrolled inflammation in familial Mediterranean fever

We report on a familial Mediterranean fever (FMF) patient homozygous for p.M694V in the MEFV gene who developed chronic myelomonocytic leukemia (CMML) leading to an uncontrolled and fatal inflammatory syndrome. Plasma levels of IL-6 and IL-18 were found to be very high, as compared to healthy contro...

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Detalles Bibliográficos
Autores principales:	Awad, Fawaz, Georgin-Lavialle, Sophie, Brignier, Anne, Derrieux, Coralie, Aouba, Achille, Stankovic-Stojanovic, Katia, Grateau, Gilles, Amselem, Serge, Hermine, Olivier, Karabina, Sonia-Athina
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2015
Materias:	Letter to the Editor
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4485869/ https://www.ncbi.nlm.nih.gov/pubmed/26076658 http://dx.doi.org/10.1186/s13023-015-0295-9

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