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A Fine Balance of Dietary Lipids Improves Pathology of a Murine Model of VCP-Associated Multisystem Proteinopathy
The discovery of effective therapies and of disease mechanisms underlying valosin containing protein (VCP)-associated myopathies and neurodegenerative disorders remains elusive. VCP disease, caused by mutations in the VCP gene, are a clinically and genetically heterogeneous group of disorders with m...
Autores principales: | Llewellyn, Katrina J., Walker, Naomi, Nguyen, Christopher, Tan, Baichang, BenMohamed, Lbachir, Kimonis, Virginia E., Nalbandian, Angèle |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4489713/ https://www.ncbi.nlm.nih.gov/pubmed/26134519 http://dx.doi.org/10.1371/journal.pone.0131995 |
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