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Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child

Fibromatosis also known as desmoid tumor is an uncommon cause of a mediastinal mass in patients of all ages. Imaging appearance of fibromatosis is generally nonspecific and demands special attention to subtle details to be correctly identified as a possibility. Management of the patient is often com...

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Autores principales: Bhat, Venkatraman, Raju, Praveen, Rao, Sanjay, Ramaiah, Srinivas
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4490575/
https://www.ncbi.nlm.nih.gov/pubmed/26180657
http://dx.doi.org/10.4103/2156-7514.159452
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author Bhat, Venkatraman
Raju, Praveen
Rao, Sanjay
Ramaiah, Srinivas
author_facet Bhat, Venkatraman
Raju, Praveen
Rao, Sanjay
Ramaiah, Srinivas
author_sort Bhat, Venkatraman
collection PubMed
description Fibromatosis also known as desmoid tumor is an uncommon cause of a mediastinal mass in patients of all ages. Imaging appearance of fibromatosis is generally nonspecific and demands special attention to subtle details to be correctly identified as a possibility. Management of the patient is often complicated by failure to obtain precise pre-operative diagnosis. Location of a mass in the anterior mediastinum with encasement of vital structures is not favourable for complete cure. Although histologically benign, biological behaviour of the lesion varies between benign fibrous proliferation and low-grade fibrosarcoma. We present imaging appearances, surgical management dilemma, and the histopathological details of a case of fibromatosis in the anterior mediastinum in a child.
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spelling pubmed-44905752015-07-15 Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child Bhat, Venkatraman Raju, Praveen Rao, Sanjay Ramaiah, Srinivas J Clin Imaging Sci Case Report Fibromatosis also known as desmoid tumor is an uncommon cause of a mediastinal mass in patients of all ages. Imaging appearance of fibromatosis is generally nonspecific and demands special attention to subtle details to be correctly identified as a possibility. Management of the patient is often complicated by failure to obtain precise pre-operative diagnosis. Location of a mass in the anterior mediastinum with encasement of vital structures is not favourable for complete cure. Although histologically benign, biological behaviour of the lesion varies between benign fibrous proliferation and low-grade fibrosarcoma. We present imaging appearances, surgical management dilemma, and the histopathological details of a case of fibromatosis in the anterior mediastinum in a child. Medknow Publications & Media Pvt Ltd 2015-06-29 /pmc/articles/PMC4490575/ /pubmed/26180657 http://dx.doi.org/10.4103/2156-7514.159452 Text en Copyright: © Journal of Clinical Imaging Science http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Bhat, Venkatraman
Raju, Praveen
Rao, Sanjay
Ramaiah, Srinivas
Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child
title Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child
title_full Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child
title_fullStr Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child
title_full_unstemmed Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child
title_short Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child
title_sort infantile fibromatosis: a rare cause of anterior mediastinal mass in a child
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4490575/
https://www.ncbi.nlm.nih.gov/pubmed/26180657
http://dx.doi.org/10.4103/2156-7514.159452
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