Cargando…
Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child
Fibromatosis also known as desmoid tumor is an uncommon cause of a mediastinal mass in patients of all ages. Imaging appearance of fibromatosis is generally nonspecific and demands special attention to subtle details to be correctly identified as a possibility. Management of the patient is often com...
Autores principales: | , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2015
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4490575/ https://www.ncbi.nlm.nih.gov/pubmed/26180657 http://dx.doi.org/10.4103/2156-7514.159452 |
_version_ | 1782379533557563392 |
---|---|
author | Bhat, Venkatraman Raju, Praveen Rao, Sanjay Ramaiah, Srinivas |
author_facet | Bhat, Venkatraman Raju, Praveen Rao, Sanjay Ramaiah, Srinivas |
author_sort | Bhat, Venkatraman |
collection | PubMed |
description | Fibromatosis also known as desmoid tumor is an uncommon cause of a mediastinal mass in patients of all ages. Imaging appearance of fibromatosis is generally nonspecific and demands special attention to subtle details to be correctly identified as a possibility. Management of the patient is often complicated by failure to obtain precise pre-operative diagnosis. Location of a mass in the anterior mediastinum with encasement of vital structures is not favourable for complete cure. Although histologically benign, biological behaviour of the lesion varies between benign fibrous proliferation and low-grade fibrosarcoma. We present imaging appearances, surgical management dilemma, and the histopathological details of a case of fibromatosis in the anterior mediastinum in a child. |
format | Online Article Text |
id | pubmed-4490575 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2015 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-44905752015-07-15 Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child Bhat, Venkatraman Raju, Praveen Rao, Sanjay Ramaiah, Srinivas J Clin Imaging Sci Case Report Fibromatosis also known as desmoid tumor is an uncommon cause of a mediastinal mass in patients of all ages. Imaging appearance of fibromatosis is generally nonspecific and demands special attention to subtle details to be correctly identified as a possibility. Management of the patient is often complicated by failure to obtain precise pre-operative diagnosis. Location of a mass in the anterior mediastinum with encasement of vital structures is not favourable for complete cure. Although histologically benign, biological behaviour of the lesion varies between benign fibrous proliferation and low-grade fibrosarcoma. We present imaging appearances, surgical management dilemma, and the histopathological details of a case of fibromatosis in the anterior mediastinum in a child. Medknow Publications & Media Pvt Ltd 2015-06-29 /pmc/articles/PMC4490575/ /pubmed/26180657 http://dx.doi.org/10.4103/2156-7514.159452 Text en Copyright: © Journal of Clinical Imaging Science http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Bhat, Venkatraman Raju, Praveen Rao, Sanjay Ramaiah, Srinivas Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child |
title | Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child |
title_full | Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child |
title_fullStr | Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child |
title_full_unstemmed | Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child |
title_short | Infantile Fibromatosis: A Rare Cause of Anterior Mediastinal Mass in a Child |
title_sort | infantile fibromatosis: a rare cause of anterior mediastinal mass in a child |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4490575/ https://www.ncbi.nlm.nih.gov/pubmed/26180657 http://dx.doi.org/10.4103/2156-7514.159452 |
work_keys_str_mv | AT bhatvenkatraman infantilefibromatosisararecauseofanteriormediastinalmassinachild AT rajupraveen infantilefibromatosisararecauseofanteriormediastinalmassinachild AT raosanjay infantilefibromatosisararecauseofanteriormediastinalmassinachild AT ramaiahsrinivas infantilefibromatosisararecauseofanteriormediastinalmassinachild |