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A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation

Sinus histiocytosis with massive lymphadenopathy (SHML) or Rosai–Dorfman disease is a non-neoplastic condition which typically presents as massive, bilateral cervical lymphadenopathy and can involve multiple extranodal organ systems such as skin, eyes, and upper respiratory tract in about 28% cases....

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Autores principales: Patel, Maharshi H, Jambhekar, Kedar R, Pandey, Tarun, Ram, Roopa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4531454/
https://www.ncbi.nlm.nih.gov/pubmed/26288524
http://dx.doi.org/10.4103/0971-3026.161459
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author Patel, Maharshi H
Jambhekar, Kedar R
Pandey, Tarun
Ram, Roopa
author_facet Patel, Maharshi H
Jambhekar, Kedar R
Pandey, Tarun
Ram, Roopa
author_sort Patel, Maharshi H
collection PubMed
description Sinus histiocytosis with massive lymphadenopathy (SHML) or Rosai–Dorfman disease is a non-neoplastic condition which typically presents as massive, bilateral cervical lymphadenopathy and can involve multiple extranodal organ systems such as skin, eyes, and upper respiratory tract in about 28% cases. Bone lesions in association with nodal disease are seen in less than 10% cases. Isolated bone involvement as the only manifestation of SHML is extremely rare, with less than 50 cases reported in the literature. We report a very uncommon case of Rosai–Dorfman disease with isolated multifocal osseous involvement as the only presenting feature, involving about 10 different sites with no lymphadenopathy or other organ system involvement.
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spelling pubmed-45314542015-08-18 A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation Patel, Maharshi H Jambhekar, Kedar R Pandey, Tarun Ram, Roopa Indian J Radiol Imaging Musculoskeletal Radiology Sinus histiocytosis with massive lymphadenopathy (SHML) or Rosai–Dorfman disease is a non-neoplastic condition which typically presents as massive, bilateral cervical lymphadenopathy and can involve multiple extranodal organ systems such as skin, eyes, and upper respiratory tract in about 28% cases. Bone lesions in association with nodal disease are seen in less than 10% cases. Isolated bone involvement as the only manifestation of SHML is extremely rare, with less than 50 cases reported in the literature. We report a very uncommon case of Rosai–Dorfman disease with isolated multifocal osseous involvement as the only presenting feature, involving about 10 different sites with no lymphadenopathy or other organ system involvement. Medknow Publications & Media Pvt Ltd 2015 /pmc/articles/PMC4531454/ /pubmed/26288524 http://dx.doi.org/10.4103/0971-3026.161459 Text en Copyright: © Indian Journal of Radiology and Imaging http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Musculoskeletal Radiology
Patel, Maharshi H
Jambhekar, Kedar R
Pandey, Tarun
Ram, Roopa
A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation
title A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation
title_full A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation
title_fullStr A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation
title_full_unstemmed A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation
title_short A rare case of extra nodal Rosai-Dorfman disease with isolated multifocal osseous manifestation
title_sort rare case of extra nodal rosai-dorfman disease with isolated multifocal osseous manifestation
topic Musculoskeletal Radiology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4531454/
https://www.ncbi.nlm.nih.gov/pubmed/26288524
http://dx.doi.org/10.4103/0971-3026.161459
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