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Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis

We report a 46-year-old woman with primary biliary cirrhosis (PBC) presenting with Sjögren’s syndrome and systemic mononuclear inflammatory vasculopathy. Biopsy specimens of sural nerve showed findings consistent with vasculitic neuropathy. Perivascular inflammatory mononuclear cell infiltration was...

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Autores principales: Min, Jun-Ki, Park, Kyung-Soo, Yu, Won-Jong, Lee, Youn-Soo, Park, Sung-Min, Park, Sung-Hwan, Cho, Chul-Soo, Kim, Ho-Youn
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Korean Association of Internal Medicine 2000
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4531751/
https://www.ncbi.nlm.nih.gov/pubmed/10714099
http://dx.doi.org/10.3904/kjim.2000.15.1.89
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author Min, Jun-Ki
Park, Kyung-Soo
Yu, Won-Jong
Lee, Youn-Soo
Park, Sung-Min
Park, Sung-Hwan
Cho, Chul-Soo
Kim, Ho-Youn
author_facet Min, Jun-Ki
Park, Kyung-Soo
Yu, Won-Jong
Lee, Youn-Soo
Park, Sung-Min
Park, Sung-Hwan
Cho, Chul-Soo
Kim, Ho-Youn
author_sort Min, Jun-Ki
collection PubMed
description We report a 46-year-old woman with primary biliary cirrhosis (PBC) presenting with Sjögren’s syndrome and systemic mononuclear inflammatory vasculopathy. Biopsy specimens of sural nerve showed findings consistent with vasculitic neuropathy. Perivascular inflammatory mononuclear cell infiltration was observed on muscle biopsy specimen. The findings of abdominal computed tomography and brain magnetic resonance imaging were suggestive of vasculitis. Clinical manifestations and radiologic findings were improved after high dose prednisolone therapy.
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spelling pubmed-45317512015-10-02 Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis Min, Jun-Ki Park, Kyung-Soo Yu, Won-Jong Lee, Youn-Soo Park, Sung-Min Park, Sung-Hwan Cho, Chul-Soo Kim, Ho-Youn Korean J Intern Med Articles We report a 46-year-old woman with primary biliary cirrhosis (PBC) presenting with Sjögren’s syndrome and systemic mononuclear inflammatory vasculopathy. Biopsy specimens of sural nerve showed findings consistent with vasculitic neuropathy. Perivascular inflammatory mononuclear cell infiltration was observed on muscle biopsy specimen. The findings of abdominal computed tomography and brain magnetic resonance imaging were suggestive of vasculitis. Clinical manifestations and radiologic findings were improved after high dose prednisolone therapy. Korean Association of Internal Medicine 2000-01 /pmc/articles/PMC4531751/ /pubmed/10714099 http://dx.doi.org/10.3904/kjim.2000.15.1.89 Text en Copyright © 2000 The Korean Association of Internal Medicine This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted noncommercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Articles
Min, Jun-Ki
Park, Kyung-Soo
Yu, Won-Jong
Lee, Youn-Soo
Park, Sung-Min
Park, Sung-Hwan
Cho, Chul-Soo
Kim, Ho-Youn
Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis
title Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis
title_full Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis
title_fullStr Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis
title_full_unstemmed Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis
title_short Systemic Mononuclear Inflammatory Vasculopathy Associated with Sjögren’s Syndrome in a Patient with Primary Biliary Cirrhosis
title_sort systemic mononuclear inflammatory vasculopathy associated with sjögren’s syndrome in a patient with primary biliary cirrhosis
topic Articles
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4531751/
https://www.ncbi.nlm.nih.gov/pubmed/10714099
http://dx.doi.org/10.3904/kjim.2000.15.1.89
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