Secondary Renal Amyloidosis in Adult Onset Still’s Disease: Case report and Review of the Literature

We report a 25-year-old Korean woman with Adult onset Still’s disease (AOSD) presented with renal amyloidosis, which had developed four years after disease onset. We successfully treated her with prednisolone, colchicine and cyclophosphamide. A review of the literature uncovered about 10 cases, most...

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Detalles Bibliográficos
Autores principales: Oh, Young Bae, Bae, Sang-Cheol, Jung, Ja-Hun, Kim, Tae-Hwan, Jun, Jae-Bum, Jung, Sung-Soo, Lee, In-Hong, Yoo, Dae-Hyun, Park, Moon Hyang, Kim, Seong Yoon
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Korean Association of Internal Medicine 2000
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4531753/
https://www.ncbi.nlm.nih.gov/pubmed/10992726
http://dx.doi.org/10.3904/kjim.2000.15.2.131
Descripción
Sumario:We report a 25-year-old Korean woman with Adult onset Still’s disease (AOSD) presented with renal amyloidosis, which had developed four years after disease onset. We successfully treated her with prednisolone, colchicine and cyclophosphamide. A review of the literature uncovered about 10 cases, most of which were treated by various regimens that resulted in poor outcomes. Renal amyloidosis should be suspected in patients with AOSD who have unexplained proteinuria. Although the mechanism of renal amyloid deposition is not well known, earlier histopathologic diagnosis and choice of regimen may affect prognosis.

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