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Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation

This paper presents the case of a young girl with idiopathic pulmonary hypertension, who developed signs of severe heart failure within a short period of time. Pharmacotherapy with sildenafil and bosentan (among other drugs) was ineffective. Heart catheterization revealed suprasystemic pressure in t...

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Autores principales: Fiszer, Roland, Karwot, Blandyna, Chodór, Beata, Szkutnik, Małgorzata, Kobylarz, Krzysztof, Skalski, Janusz, Białkowski, Jacek
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Termedia Publishing House 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4550015/
https://www.ncbi.nlm.nih.gov/pubmed/26336504
http://dx.doi.org/10.5114/kitp.2015.52864
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author Fiszer, Roland
Karwot, Blandyna
Chodór, Beata
Szkutnik, Małgorzata
Kobylarz, Krzysztof
Skalski, Janusz
Białkowski, Jacek
author_facet Fiszer, Roland
Karwot, Blandyna
Chodór, Beata
Szkutnik, Małgorzata
Kobylarz, Krzysztof
Skalski, Janusz
Białkowski, Jacek
author_sort Fiszer, Roland
collection PubMed
description This paper presents the case of a young girl with idiopathic pulmonary hypertension, who developed signs of severe heart failure within a short period of time. Pharmacotherapy with sildenafil and bosentan (among other drugs) was ineffective. Heart catheterization revealed suprasystemic pressure in the pulmonary artery. At the age of 7.5 years, the patient underwent a surgical Potts shunt (namely, a direct side-by-side anastomosis from the left pulmonary artery to the descending aorta). The procedure resulted in a significant improvement of the clinical, echocardiographic, and biochemical parameters, which persists after one and a half years of follow-up. After the surgery, pharmacotherapy with bosentan was gradually discontinued.
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spelling pubmed-45500152015-09-02 Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation Fiszer, Roland Karwot, Blandyna Chodór, Beata Szkutnik, Małgorzata Kobylarz, Krzysztof Skalski, Janusz Białkowski, Jacek Kardiochir Torakochirurgia Pol Case Reports This paper presents the case of a young girl with idiopathic pulmonary hypertension, who developed signs of severe heart failure within a short period of time. Pharmacotherapy with sildenafil and bosentan (among other drugs) was ineffective. Heart catheterization revealed suprasystemic pressure in the pulmonary artery. At the age of 7.5 years, the patient underwent a surgical Potts shunt (namely, a direct side-by-side anastomosis from the left pulmonary artery to the descending aorta). The procedure resulted in a significant improvement of the clinical, echocardiographic, and biochemical parameters, which persists after one and a half years of follow-up. After the surgery, pharmacotherapy with bosentan was gradually discontinued. Termedia Publishing House 2015-06-30 2015-06 /pmc/articles/PMC4550015/ /pubmed/26336504 http://dx.doi.org/10.5114/kitp.2015.52864 Text en Copyright © 2015 http://creativecommons.org/licenses/by-nc-nd/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-Noncommercial 3.0 Unported License, permitting all non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Fiszer, Roland
Karwot, Blandyna
Chodór, Beata
Szkutnik, Małgorzata
Kobylarz, Krzysztof
Skalski, Janusz
Białkowski, Jacek
Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation
title Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation
title_full Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation
title_fullStr Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation
title_full_unstemmed Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation
title_short Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation
title_sort potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4550015/
https://www.ncbi.nlm.nih.gov/pubmed/26336504
http://dx.doi.org/10.5114/kitp.2015.52864
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