Rare occurrence of intracranial epidermoid tumor in an unusual location with atypical radiological features

Intracranial epidermoid tumors are benign rare tumors that arise due to dysembryogenesis. Thought rare, they have characteristic radiological features such as their magnetic resonance imaging signal intensities and a typical location. We present a rare case of intracranial epidermoid tumor in a young female patient that was unusually located within the left frontal lobe and had certain atypical radiological findings. Preoperatively, this lesion was erroneously presumed to be a low grade glioma or a dermoid. Therefore, this case report prompts us to include atypical epidermoid cyst in the list of differential diagnosis for nonenhancing lobar tumors.