Cardiac involvement in Erdheim- Chester disease: MRI findings and literature revision

Erdheim-Chester disease (ECD) is a rare form of non-Langerhans cell histiocytosis, characterized by the involvement of several organs. The lesions may be skeletal or extra-skeletal: in particular, long bones, skin, lungs, and the cardiovascular and the central nervous systems can be affected. In thi...

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Detalles Bibliográficos
Autores principales: Ponsiglione, Andrea, Puglia, Marta, Barbuto, Luigi, Solla, Raffaele, Altiero, Michele, Lubrano, Valentina, Imbriaco, Massimo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SAGE Publications 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4563377/
https://www.ncbi.nlm.nih.gov/pubmed/26405559
http://dx.doi.org/10.1177/2058460115592273
Descripción
Sumario:Erdheim-Chester disease (ECD) is a rare form of non-Langerhans cell histiocytosis, characterized by the involvement of several organs. The lesions may be skeletal or extra-skeletal: in particular, long bones, skin, lungs, and the cardiovascular and the central nervous systems can be affected. In this report, we describe a case of a 34-year-old man, who came to our observation with symptomatic ECD, for a correct assessment of the degree of cardiac involvement through magnetic resonance imaging (MRI).

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