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Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association

Behcet's disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet's disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior ven...

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Autores principales: Batur, Abdussamet, Dorum, Meltem, Yüksekkaya, Hasan Ali, Koc, Osman
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4594976/
https://www.ncbi.nlm.nih.gov/pubmed/26491527
http://dx.doi.org/10.11604/pamj.2015.21.84.3917
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author Batur, Abdussamet
Dorum, Meltem
Yüksekkaya, Hasan Ali
Koc, Osman
author_facet Batur, Abdussamet
Dorum, Meltem
Yüksekkaya, Hasan Ali
Koc, Osman
author_sort Batur, Abdussamet
collection PubMed
description Behcet's disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet's disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior vena cava is rare among the arteries and veins, respectively. When disease affect the veins, it is in the form of thrombosis. Arterial complications include aneurysms, stenosis and occlusions. Both rupture of arterial aneurysm and occlusion of suprahepatic veins, causing Budd-Chiari syndrome, are associated with a high mortality rate. Vascular involvement is more common in male patients than in female patients. Men and patients with a younger age of onset present with a more severe prognosis. In this case report, we describe a very rare cause of intrarenal arterial aneurysm's rupture with previous Budd-Chiari syndrome due to Behcet's disease and successful angiographic embolization of actively bleeding aneurysm.
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spelling pubmed-45949762015-10-21 Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association Batur, Abdussamet Dorum, Meltem Yüksekkaya, Hasan Ali Koc, Osman Pan Afr Med J Case Report Behcet's disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet's disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior vena cava is rare among the arteries and veins, respectively. When disease affect the veins, it is in the form of thrombosis. Arterial complications include aneurysms, stenosis and occlusions. Both rupture of arterial aneurysm and occlusion of suprahepatic veins, causing Budd-Chiari syndrome, are associated with a high mortality rate. Vascular involvement is more common in male patients than in female patients. Men and patients with a younger age of onset present with a more severe prognosis. In this case report, we describe a very rare cause of intrarenal arterial aneurysm's rupture with previous Budd-Chiari syndrome due to Behcet's disease and successful angiographic embolization of actively bleeding aneurysm. The African Field Epidemiology Network 2015-06-03 /pmc/articles/PMC4594976/ /pubmed/26491527 http://dx.doi.org/10.11604/pamj.2015.21.84.3917 Text en © Abdussamet Batur et al. http://creativecommons.org/licenses/by/2.0/ The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Batur, Abdussamet
Dorum, Meltem
Yüksekkaya, Hasan Ali
Koc, Osman
Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
title Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
title_full Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
title_fullStr Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
title_full_unstemmed Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
title_short Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
title_sort budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4594976/
https://www.ncbi.nlm.nih.gov/pubmed/26491527
http://dx.doi.org/10.11604/pamj.2015.21.84.3917
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