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Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association
Behcet's disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet's disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior ven...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The African Field Epidemiology Network
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4594976/ https://www.ncbi.nlm.nih.gov/pubmed/26491527 http://dx.doi.org/10.11604/pamj.2015.21.84.3917 |
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author | Batur, Abdussamet Dorum, Meltem Yüksekkaya, Hasan Ali Koc, Osman |
author_facet | Batur, Abdussamet Dorum, Meltem Yüksekkaya, Hasan Ali Koc, Osman |
author_sort | Batur, Abdussamet |
collection | PubMed |
description | Behcet's disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet's disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior vena cava is rare among the arteries and veins, respectively. When disease affect the veins, it is in the form of thrombosis. Arterial complications include aneurysms, stenosis and occlusions. Both rupture of arterial aneurysm and occlusion of suprahepatic veins, causing Budd-Chiari syndrome, are associated with a high mortality rate. Vascular involvement is more common in male patients than in female patients. Men and patients with a younger age of onset present with a more severe prognosis. In this case report, we describe a very rare cause of intrarenal arterial aneurysm's rupture with previous Budd-Chiari syndrome due to Behcet's disease and successful angiographic embolization of actively bleeding aneurysm. |
format | Online Article Text |
id | pubmed-4594976 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2015 |
publisher | The African Field Epidemiology Network |
record_format | MEDLINE/PubMed |
spelling | pubmed-45949762015-10-21 Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association Batur, Abdussamet Dorum, Meltem Yüksekkaya, Hasan Ali Koc, Osman Pan Afr Med J Case Report Behcet's disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet's disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior vena cava is rare among the arteries and veins, respectively. When disease affect the veins, it is in the form of thrombosis. Arterial complications include aneurysms, stenosis and occlusions. Both rupture of arterial aneurysm and occlusion of suprahepatic veins, causing Budd-Chiari syndrome, are associated with a high mortality rate. Vascular involvement is more common in male patients than in female patients. Men and patients with a younger age of onset present with a more severe prognosis. In this case report, we describe a very rare cause of intrarenal arterial aneurysm's rupture with previous Budd-Chiari syndrome due to Behcet's disease and successful angiographic embolization of actively bleeding aneurysm. The African Field Epidemiology Network 2015-06-03 /pmc/articles/PMC4594976/ /pubmed/26491527 http://dx.doi.org/10.11604/pamj.2015.21.84.3917 Text en © Abdussamet Batur et al. http://creativecommons.org/licenses/by/2.0/ The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Batur, Abdussamet Dorum, Meltem Yüksekkaya, Hasan Ali Koc, Osman Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association |
title | Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association |
title_full | Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association |
title_fullStr | Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association |
title_full_unstemmed | Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association |
title_short | Budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association |
title_sort | budd-chiari syndrome and renal arterial neurysms due to behcet disease: a rare association |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4594976/ https://www.ncbi.nlm.nih.gov/pubmed/26491527 http://dx.doi.org/10.11604/pamj.2015.21.84.3917 |
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